PMID- 10021793 OWN - NLM STAT- MEDLINE DCOM- 19990309 LR - 20161124 IS - 0870-399X (Print) IS - 0870-399X (Linking) VI - 11 IP - 11 DP - 1998 Nov TI - [Congenital bronchopulmonary cystic disease]. PG - 947-52 AB - From September 1989 to December 1994, 12 children with congenital bronchopulmonary cystic disease were operated in the Department of Pediatric Surgery, Santa Maria Hospital. Four cases of bronchogenic cyst (BC), 2 of cystic adenomatoid malformation (CAM), 3 of pulmonary sequestration (PS), and 3 of congenital lobar emphysema (CLE) were found. Age ranged between 9 days and 10 years without predominance of gender. Seven were younger than one year of age, of which 5 were less than 6 months old at the time of surgery. The CAT scan was most useful in the diagnosis and follow-up of these children. The review of these cases helped evaluate our experience in the diagnosis and surgical approach for these congenital malformations. Successful treatment depends on early diagnosis and the planning of therapeutic priorities, based on the embryological and pathophysiological knowledge at these anomalies. The embryological mechanisms implicated in the development are discussed and the results of surgical treatment are presented. FAU - Mendes, J AU - Mendes J AD - Unidade de Cirurgia Pediatrica, Hospital de Santa Maria, Lisboa. FAU - Martins, V AU - Martins V FAU - Goncalves, M AU - Goncalves M LA - por PT - Journal Article TT - Doenca quistica congenita bronco-pulmonar. PL - Portugal TA - Acta Med Port JT - Acta medica portuguesa JID - 7906803 SB - IM MH - Bronchogenic Cyst/congenital/diagnostic imaging/*surgery MH - Child MH - Cystic Adenomatoid Malformation of Lung, Congenital/diagnostic imaging/*surgery MH - Female MH - Humans MH - Infant MH - Infant, Newborn MH - Lung/diagnostic imaging MH - Male MH - Pulmonary Emphysema/congenital/diagnostic imaging/*surgery MH - Retrospective Studies MH - Tomography, X-Ray Computed EDAT- 1999/02/18 00:00 MHDA- 1999/02/18 00:01 CRDT- 1999/02/18 00:00 PHST- 1999/02/18 00:00 [pubmed] PHST- 1999/02/18 00:01 [medline] PHST- 1999/02/18 00:00 [entrez] PST - ppublish SO - Acta Med Port. 1998 Nov;11(11):947-52.