PMID- 10909281
OWN - NLM
STAT- MEDLINE
DCOM- 20001019
LR  - 20071115
IS  - 0033-2240 (Print)
IS  - 0033-2240 (Linking)
VI  - 57
IP  - 3
DP  - 2000
TI  - [Operative outcome in children with total anomalous pulmonary venous connection].
PG  - 139-42
AB  - The authors present their experience in surgical treatment of children with total 
      anomalous pulmonary venous connection. A retrospective analysis was carried out 
      in 42 patients operated on in the years 1979-1999. The group included 30 boys 
      aged 7 days to 7 years (mean 170 +/- 480 days) and 12 girls aged 14 days to 7 
      months (mean 86 +/- 80 days). Diagnostic studies allowed to determine that 24 
      patients (57%) had supracardiac type (type I), nine (21%)--cardiac (type II), 
      five (12%)--infracardiac (type III) and four (10%)--mixed (type IV). The 
      diagnosis was based on clinical examinations and echocardiography, supplemented 
      in 17 patients (40%) by hemodynamic studies and angiocardiography. Preoperative 
      pulmonary hypertension was noted in 34 children (81%), including 15 patients 
      (36%) diagnosed by hemodynamic studies and 19 children (45%) by echocardiography. 
      All children were operated on in deep hypothermia with circulatory arrest. In the 
      early postoperative period (30 days), seven children (17%) died, while four more 
      (9.5%) died in the latter period. The former were characterized by significantly 
      lower birth weight values (p = 0.023). The total mortality rate was higher in 
      children with type II and III anomalies. No statistically significant association 
      was found between preoperative pulmonary hypertension and early mortality. 
      Thirty-one children (74%) remain in late follow-up. All of them are in NYHA (New 
      York Heart Association) class I and develop normally. Total anomalous pulmonary 
      venous connection is a rare congenital anomaly that can be fully repaired with 
      improving early and late results.
FAU - Malec, E
AU  - Malec E
AD  - Klinika Kardiochirurgii Dzieciecej Katedry Chirurgii Pediatrycznej, Uniwersytetu 
      Jagiellonskiego w Krakowie. mimalec@cyf-kr.edu.pl
FAU - Kolcz, J
AU  - Kolcz J
FAU - Januszewska, K
AU  - Januszewska K
FAU - Pajak, J
AU  - Pajak J
FAU - Mroczek, T
AU  - Mroczek T
LA  - pol
PT  - English Abstract
PT  - Journal Article
TT  - Wyniki operacyjnego leczenia dzieci z calkowitym nieprawidlowym polaczeniem zyl 
      plucnych.
PL  - Poland
TA  - Przegl Lek
JT  - Przeglad lekarski
JID - 19840720R
SB  - IM
MH  - Angiography
MH  - Cardiac Surgical Procedures
MH  - Child, Preschool
MH  - Echocardiography
MH  - Female
MH  - Follow-Up Studies
MH  - Hemodynamics
MH  - Humans
MH  - Hypothermia, Induced
MH  - Infant
MH  - Infant, Newborn
MH  - Male
MH  - Postoperative Complications/mortality
MH  - Pulmonary Veins/*abnormalities/*surgery
MH  - Retrospective Studies
MH  - Survival Rate
EDAT- 2000/07/26 11:00
MHDA- 2000/10/21 11:01
CRDT- 2000/07/26 11:00
PHST- 2000/07/26 11:00 [pubmed]
PHST- 2000/10/21 11:01 [medline]
PHST- 2000/07/26 11:00 [entrez]
PST - ppublish
SO  - Przegl Lek. 2000;57(3):139-42.