PMID- 11372614
OWN - NLM
STAT- MEDLINE
DCOM- 20020213
LR  - 20200330
IS  - 0938-7994 (Print)
IS  - 0938-7994 (Linking)
VI  - 11
IP  - 5
DP  - 2001
TI  - Bare lymphocyte syndrome: imaging findings in an adult.
PG  - 815-8
AB  - Bare lymphocyte syndrome (BLS) is a rare primary immune disorder characterized by 
      defective expression of human leukocyte antigen (HLA) on lymphocytes, often 
      resulting in extensive and recurrent multi-organ infections. We describe a 
      previously undiagnosed case of an adult woman who presented with radiological 
      findings of severe bronchiectases, near-total granulomatous destruction of facial 
      bones, and osteomyelitis. Diagnosis of BLS should be considered when evaluating 
      children with unexplained bronchiectases or adults with long history of chronic 
      multi-organ infections.
FAU - Bernaerts, A
AU  - Bernaerts A
AD  - Department of Radiology, Universitair Ziekenhuis Antwerpen Wilrijkstraat 10 2650 
      Edegem, Belgium.
FAU - Vandevenne, J E
AU  - Vandevenne JE
FAU - Lambert, J
AU  - Lambert J
FAU - De Clerck, L S
AU  - De Clerck LS
FAU - De Schepper, A M
AU  - De Schepper AM
LA  - eng
PT  - Case Reports
PT  - Journal Article
PL  - Germany
TA  - Eur Radiol
JT  - European radiology
JID - 9114774
SB  - IM
MH  - Female
MH  - Humans
MH  - Magnetic Resonance Imaging
MH  - Middle Aged
MH  - Severe Combined Immunodeficiency/*diagnostic imaging/*pathology
MH  - Tomography, X-Ray Computed
EDAT- 2001/05/25 10:00
MHDA- 2002/02/14 10:01
CRDT- 2001/05/25 10:00
PHST- 2001/05/25 10:00 [pubmed]
PHST- 2002/02/14 10:01 [medline]
PHST- 2001/05/25 10:00 [entrez]
AID - 10.1007/s003300000706 [doi]
PST - ppublish
SO  - Eur Radiol. 2001;11(5):815-8. doi: 10.1007/s003300000706.