PMID- 15229777
OWN - NLM
STAT- MEDLINE
DCOM- 20040903
LR  - 20041117
IS  - 1221-4167 (Print)
IS  - 1221-4167 (Linking)
VI  - 13
IP  - 2
DP  - 2004 Jun
TI  - Sequential therapy in a case of extrahepatic biliary atresia associated with 
      ventricular septal defect: liver transplantation followed by surgical closure of 
      the septal defect.
PG  - 125-8
AB  - Patients with extrahepatic biliary atresia (EHBA), the commonest indication for 
      liver transplantation in pediatric cases, may have associated congenital 
      anomalies, e.g. interventricular septal defect (IVSD). Even if there is a well 
      established therapeutical algorithm for a ventricular septal defect as an 
      isolated disease, the surgical approach raises special problems in a liver 
      transplanted patient. We present the case of a little girl with EHBA and IVSD. 
      The patient underwent a living related liver transplantation when she was 1 year 
      old. Persistence of the symptomatic IVSD required open heart surgery, performed 9 
      months posttransplantation. The decision to perform the closure of the IVSD was 
      difficult, yet it proved to be beneficial; the child had an uneventful 
      postoperative course, with remission of the symptoms and a good late outcome. To 
      our knowledge, this is the first case of a living-related liver transplantation 
      patient undergoing open heart surgery for IVSD closure.
FAU - Popescu, Irinel
AU  - Popescu I
AD  - Department of General Surgery and Liver Transplantation, Fundeni Clinical 
      Institute, Sos. Fundeni no. 258, 72437 Bucharest, Romania. 
      irinel.popescu@icfundeni.ro
FAU - Malago, Massimo
AU  - Malago M
FAU - Testa, Giuliano
AU  - Testa G
FAU - Ciurea, Silviu
AU  - Ciurea S
FAU - Stanescu, Codrut
AU  - Stanescu C
FAU - Socoteanu, Ion
AU  - Socoteanu I
LA  - eng
PT  - Case Reports
PT  - Journal Article
PL  - Romania
TA  - Rom J Gastroenterol
JT  - Romanian journal of gastroenterology
JID - 9315667
SB  - IM
MH  - Biliary Atresia/*surgery
MH  - Female
MH  - Heart Septal Defects, Ventricular/*surgery
MH  - Humans
MH  - Infant
MH  - *Liver Transplantation
EDAT- 2004/07/02 05:00
MHDA- 2004/09/04 05:00
CRDT- 2004/07/02 05:00
PHST- 2004/07/02 05:00 [pubmed]
PHST- 2004/09/04 05:00 [medline]
PHST- 2004/07/02 05:00 [entrez]
PST - ppublish
SO  - Rom J Gastroenterol. 2004 Jun;13(2):125-8.