PMID- 16008177
OWN - NLM
STAT- MEDLINE
DCOM- 20050729
LR  - 20090213
IS  - 0003-9683 (Print)
IS  - 0003-9683 (Linking)
VI  - 97
IP  - 10
DP  - 2004 Oct
TI  - [Congenital complete atrio-ventricular block].
PG  - 994-9
AB  - Congenital complete atrio-ventricular block is a rare condition, the result of an 
      anatomical anomaly of the conduction pathways, or even the trans-placental 
      passage of maternal antibodies causing fetal myocarditis with fibrosis of the 
      conduction tissue. It is not clear whether AV block discovered later in childhood 
      is really "congenital". Whatever the age of the child, the only treatment is 
      pacemaker implantation. Cardiac failure and syncope are absolute indications for 
      implantation. Children whose heart rate is below 50 beats per minute (bpm) 
      represent a group at high risk of syncope or even sudden death and must be paced, 
      even if asymptomatic. Moreover, certain patients with immunological complete AV 
      block have cardiopathy and must also be paced. In our department, the route for 
      pacing is epicardial in younger children, in practice weighing less than 10-15 
      kg, and endocavitary in older children. The choice is either double chamber 
      pacing, which restores AV conduction initiated by the child's sinus, or 
      ventricular pacing with activity-controlled heart rate. Although worrying 
      complications have been described, such as venous thrombosis, infections related 
      to repeated interventions, and delayed cardiomyopathy, the results of paediatric 
      pacing are generally satisfactory and the great majority of children with 
      congenital complete AV block lead a normal life.
FAU - Villain, E
AU  - Villain E
AD  - Departement de pediatrie, hopital Necker-Enfants malades, Paris. 
      elisabeth.villain@nck.ap-hop-paris.fr
LA  - fre
PT  - English Abstract
PT  - Journal Article
PT  - Review
TT  - Bloc auriculo-ventriculaire complet congenital.
PL  - France
TA  - Arch Mal Coeur Vaiss
JT  - Archives des maladies du coeur et des vaisseaux
JID - 0406011
SB  - IM
MH  - Age Factors
MH  - Body Weight
MH  - Child
MH  - Child, Preschool
MH  - Heart Block/*congenital/*therapy
MH  - Heart Rate
MH  - Humans
MH  - Infant
MH  - Infant, Newborn
MH  - *Pacemaker, Artificial
RF  - 29
EDAT- 2005/07/13 09:00
MHDA- 2005/07/30 09:00
CRDT- 2005/07/13 09:00
PHST- 2005/07/13 09:00 [pubmed]
PHST- 2005/07/30 09:00 [medline]
PHST- 2005/07/13 09:00 [entrez]
PST - ppublish
SO  - Arch Mal Coeur Vaiss. 2004 Oct;97(10):994-9.