PMID- 16321209 OWN - NLM STAT- MEDLINE DCOM- 20070608 LR - 20221207 IS - 0376-2491 (Print) IS - 0376-2491 (Linking) VI - 85 IP - 32 DP - 2005 Aug 24 TI - [Surgical treatment of the aortic root aneurysm related to Marfan syndrome]. PG - 2279-82 AB - OBJECTIVE: To review the experience of surgical treatment of aortic root aneurysm of Marfan syndrome. METHODS: We The clinical data of 84 Marfan syndrome patients, 61 males and 23 females, aged 35 +/- 12 (5 - 62), 41 cases presenting with aortic dissection (Debakey type I in 32 cases and type II in 9), 52 cases with moderate to severe aortic regurgitation, and 9 cases with moderate to severe mitral regurgitation, 43 cases with cardiac function of class I - II, 30 with class III and 11 with class IV according the New York Heart Association (NYHA) standard, who underwent surgical treatment for aortic root aneurysm with a mean diameter of 68 mm +/- 14 mm, were analyzed. Bentall procedure was performed in 68 cases, Wheat procedure in 6, Cabrol procedure in 5, and aortic valve replacement and aortoplasty in 5. Concomitant procedures included mitral value replacement and mitral valvuoplasty in 3 cases respectively. Urgent surgery was conducted in 28 cases, and elective operation in 56 cases. RESULTS: There were 3 in-hospital deaths (3.57%). 76 cases were followed up for a mean duration of 55 +/- 31 months. Three patients underwent reoperation. The cardiac function returned to class I - II except for 2 cases that remained at the class III. CONCLUSION: Bentall procedure should be the first choice of the surgery for aortic root aneurysm of Marfan syndrome with a low mortality and a good late outcome. FAU - Zheng, Si-hong AU - Zheng SH AD - Department of Cardiac surgery, Beijing Anzhen Hospital, Capital University of Medical Sciences, Beijing 100029, China. FAU - Sun, Yan-qing AU - Sun YQ FAU - Meng, Xu AU - Meng X FAU - Zhang, Hong AU - Zhang H FAU - Hou, Xiao-tong AU - Hou XT FAU - Wang, Jian-gang AU - Wang JG FAU - Gao, Feng AU - Gao F LA - chi PT - English Abstract PT - Journal Article PL - China TA - Zhonghua Yi Xue Za Zhi JT - Zhonghua yi xue za zhi JID - 7511141 SB - IM MH - Adolescent MH - Adult MH - Aortic Dissection/*etiology/*surgery MH - Aortic Aneurysm/*etiology/*surgery MH - Cardiac Surgical Procedures/methods MH - Child MH - Child, Preschool MH - Female MH - Follow-Up Studies MH - Humans MH - Male MH - Marfan Syndrome/*complications MH - Middle Aged EDAT- 2005/12/03 09:00 MHDA- 2007/06/09 09:00 CRDT- 2005/12/03 09:00 PHST- 2005/12/03 09:00 [pubmed] PHST- 2007/06/09 09:00 [medline] PHST- 2005/12/03 09:00 [entrez] PST - ppublish SO - Zhonghua Yi Xue Za Zhi. 2005 Aug 24;85(32):2279-82.