PMID- 16343800
OWN - NLM
STAT- MEDLINE
DCOM- 20060821
LR  - 20151119
IS  - 0344-0338 (Print)
IS  - 0344-0338 (Linking)
VI  - 202
IP  - 1
DP  - 2006
TI  - Perivascular epithelioid cell sarcoma (malignant PEComa) of the ileum.
PG  - 37-41
AB  - Epithelioid angiomyolipoma (AML) is the prototype of a heterogeneous group of 
      lesions characterized by the presence of HMB-45 positive cells with clear 
      cytoplasm, perivascular distribution, and combined myomelanocytic features, 
      so-called perivascular epithelioid cells (PECs). These lesions are being 
      increasingly referred to as PEComas. PEComas have been reported at diverse 
      anatomic sites, but mainly in the abdominopelvic cavity and rarely in 
      parenchymatous organs, skin, and soft tissues. Gastrointestinal (GI) PEComas are 
      exceptionally rare, with less than 10 cases documented so far. Rare examples of 
      PEComas with pleomorphic histology could have been misinterpreted as unusual 
      variants of carcinoma or sarcoma. To make a contribution to the differential 
      diagnosis of difficult-to-classify pleomorphic GI sarcomas, we report on a 
      malignant pleomorphic neoplasm with features of PEComa involving the terminal 
      ileum in a 63-year-old woman. Fourteen months after resection of the primary 
      tumor, a huge abdominopelvic recurrence was successfully resected, but no distant 
      metastases were detected. The differential diagnosis and malignancy criteria of 
      GI PEComas will be discussed.
FAU - Agaimy, A
AU  - Agaimy A
AD  - Institut fur Pathologie, Klinikum Nurnberg, Prof. Ernst-Nathan-Strasse 1, 90419 
      Nurnberg, Germany. abbas.agaimy@klinikum-nuernberg.de
FAU - Wunsch, P H
AU  - Wunsch PH
LA  - eng
PT  - Case Reports
PT  - Journal Article
DEP - 20051215
PL  - Germany
TA  - Pathol Res Pract
JT  - Pathology, research and practice
JID - 7806109
RN  - 0 (Biomarkers, Tumor)
SB  - IM
MH  - Angiomyolipoma/*diagnosis/*pathology
MH  - Biomarkers, Tumor
MH  - Diagnosis, Differential
MH  - Epithelioid Cells/pathology
MH  - Female
MH  - Humans
MH  - Ileal Neoplasms/*pathology/*surgery
MH  - Ileum/pathology
MH  - Immunohistochemistry
MH  - Middle Aged
MH  - Sarcoma/*diagnosis/*pathology
MH  - Treatment Outcome
EDAT- 2005/12/14 09:00
MHDA- 2006/08/22 09:00
CRDT- 2005/12/14 09:00
PHST- 2005/08/23 00:00 [received]
PHST- 2005/10/27 00:00 [accepted]
PHST- 2005/12/14 09:00 [pubmed]
PHST- 2006/08/22 09:00 [medline]
PHST- 2005/12/14 09:00 [entrez]
AID - S0344-0338(05)00214-1 [pii]
AID - 10.1016/j.prp.2005.10.008 [doi]
PST - ppublish
SO  - Pathol Res Pract. 2006;202(1):37-41. doi: 10.1016/j.prp.2005.10.008. Epub 2005 
      Dec 15.