PMID- 18455420
OWN - NLM
STAT- MEDLINE
DCOM- 20081204
LR  - 20191210
IS  - 1010-7940 (Print)
IS  - 1010-7940 (Linking)
VI  - 34
IP  - 1
DP  - 2008 Jul
TI  - Long-term follow-up after repair of Ebstein's anomaly.
PG  - 48-54
LID - 10.1016/j.ejcts.2008.03.048 [doi]
AB  - OBJECTIVE: We studied the long-term results of vertical plication repair of 
      Ebstein's anomaly according to Carpentier. METHODS: Between 1988 and 2007, 28 
      patients (mean age 28.8+/-15.7 years, range 4-58 years) underwent vertical 
      plication repair of Ebstein's anomaly. At operation the anomaly was classified 
      according to Carpentier. In three patients (11%) a cavopulmonary shunt was added 
      at the repair on the indication of impaired right ventricular function. RESULTS: 
      There was no operative mortality. Early mortality was 3.6% (one patient). 
      Actuarial survival and actuarial freedom from reoperation at 19 years were 96% 
      (95% CI; 96-97%) and 72% (95% CI; 53-92%), respectively. Six patients required 
      reoperation, with a successful re-repair in three patients. Mean duration of 
      follow-up was 10.7+/-6.5 years. One year postoperatively, tricuspid incompetence 
      had decreased significantly (p<0.001), as had New York Heart Association (NYHA) 
      functional class (p<0.001). In addition, exercise tolerance had increased 
      (70+/-19% to 92+/-9% of predicted values, p<0.05). Both tricuspid function and 
      NYHA functional class remained essentially unchanged at the end of follow-up, 
      indicating durable haemodynamic and functional results. CONCLUSION: This study 
      demonstrates favourable long-term results following vertical plication repair of 
      Ebstein's anomaly with low mortality, acceptable morbidity and good haemodynamic 
      and functional results.
FAU - Palmen, Meindert
AU  - Palmen M
AD  - Department of Cardiothoracic Surgery, Thoraxcentre, Erasmus Medical Centre 
      Rotterdam, Rotterdam, The Netherlands. meindert_palmen@hotmail.com 
      <meindert_palmen@hotmail.com>
FAU - de Jong, Peter L
AU  - de Jong PL
FAU - Klieverik, Loes M A
AU  - Klieverik LM
FAU - Venema, Angelique C
AU  - Venema AC
FAU - Meijboom, Folkert J
AU  - Meijboom FJ
FAU - Bogers, Ad J J C
AU  - Bogers AJ
LA  - eng
PT  - Evaluation Study
PT  - Journal Article
DEP - 20080501
PL  - Germany
TA  - Eur J Cardiothorac Surg
JT  - European journal of cardio-thoracic surgery : official journal of the European 
      Association for Cardio-thoracic Surgery
JID - 8804069
SB  - IM
MH  - Adolescent
MH  - Adult
MH  - Child
MH  - Child, Preschool
MH  - Ebstein Anomaly/diagnostic imaging/physiopathology/*surgery
MH  - Exercise Test/methods
MH  - Exercise Tolerance
MH  - Female
MH  - Follow-Up Studies
MH  - Heart Ventricles/surgery
MH  - Humans
MH  - Male
MH  - Middle Aged
MH  - Postoperative Complications
MH  - Reoperation
MH  - Survival Analysis
MH  - Treatment Outcome
MH  - Tricuspid Valve/*surgery
MH  - Tricuspid Valve Insufficiency/diagnostic imaging/physiopathology/surgery
MH  - Ultrasonography
EDAT- 2008/05/06 09:00
MHDA- 2008/12/17 09:00
CRDT- 2008/05/06 09:00
PHST- 2007/11/12 00:00 [received]
PHST- 2008/02/27 00:00 [revised]
PHST- 2008/03/21 00:00 [accepted]
PHST- 2008/05/06 09:00 [pubmed]
PHST- 2008/12/17 09:00 [medline]
PHST- 2008/05/06 09:00 [entrez]
AID - S1010-7940(08)00355-2 [pii]
AID - 10.1016/j.ejcts.2008.03.048 [doi]
PST - ppublish
SO  - Eur J Cardiothorac Surg. 2008 Jul;34(1):48-54. doi: 10.1016/j.ejcts.2008.03.048. 
      Epub 2008 May 1.