PMID- 18782694 OWN - NLM STAT- MEDLINE DCOM- 20081103 LR - 20080910 IS - 1294-9361 (Print) IS - 1294-9361 (Linking) VI - 10 IP - 3 DP - 2008 Sep TI - Absence status epilepticus in monozygotic twins with Jeavons syndrome. PG - 227-30 LID - 10.1684/epd.2008.0206 [doi] AB - As a generalized form of nonconvulsive status epilepticus (NCSE), absence status epilepticus is the most common form. It manifests as prolonged, confusional states of varying severity, and continuous or repetitive generalized discharges of spikes, multiple spikes, and slow waves on EEG. Jeavons syndrome (JS) is a new type of epilepsy syndrome. Hitherto, only four sets of monozygotic twin with JS have been reported. Absence status epilepticus occurring in monozygotic twins with JS have not been reported. Here we report on monozygotic male twins of Chinese origin with JS. Both of them presented with status epilepticus with eyelid myoclonia and absences. FAU - Yang, Tianhua AU - Yang T AD - Department of Neurology, West China Hospital, Si Chuan University, Chengdu, Sichuan, PR China. FAU - Liu, Yonghong AU - Liu Y FAU - Liu, Ling AU - Liu L FAU - Yan, Bo AU - Yan B FAU - Zhang, Qin AU - Zhang Q FAU - Zhou, Dong AU - Zhou D LA - eng PT - Case Reports PT - Journal Article PL - United States TA - Epileptic Disord JT - Epileptic disorders : international epilepsy journal with videotape JID - 100891853 SB - IM MH - Adolescent MH - Electroencephalography MH - Epilepsy, Absence/*etiology/genetics/psychology MH - Humans MH - Male MH - Photosensitivity Disorders/genetics/physiopathology MH - Status Epilepticus/*etiology/genetics/psychology MH - Syndrome MH - Twins, Monozygotic EDAT- 2008/09/11 09:00 MHDA- 2008/11/04 09:00 CRDT- 2008/09/11 09:00 PHST- 2008/02/04 00:00 [received] PHST- 2008/07/03 00:00 [accepted] PHST- 2008/09/11 09:00 [pubmed] PHST- 2008/11/04 09:00 [medline] PHST- 2008/09/11 09:00 [entrez] AID - epd.2008.0206 [pii] AID - 10.1684/epd.2008.0206 [doi] PST - ppublish SO - Epileptic Disord. 2008 Sep;10(3):227-30. doi: 10.1684/epd.2008.0206.