PMID- 19242304
OWN - NLM
STAT- MEDLINE
DCOM- 20090616
LR  - 20161125
IS  - 1536-0237 (Electronic)
IS  - 0883-5993 (Linking)
VI  - 24
IP  - 1
DP  - 2009 Feb
TI  - Proteus syndrome: high-resolution CT and CT pulmonary densitovolumetry findings.
PG  - 45-8
LID - 10.1097/RTI.0b013e31818b20cd [doi]
AB  - Cystic transformation of the lungs in Proteus syndrome is considered an important 
      manifestation of this disease. We describe a case of an 11-year-old girl with a 
      diagnosis of Proteus syndrome with lung involvement. Low-dose multidetector 
      computed tomography (CT) revealed extensive diffuse cystic lung disease with left 
      lung predominance, affecting mostly the lower lung zones. The cystic lesions had 
      various sizes and variable wall thickness. Postprocessing using CT histogram 
      densitometric volumetry software (CT densitovolumetry), using the threshold -950 
      Houndsfield units (HU) for quantifying emphysema, revealed that 31% of her total 
      lung volume was composed of areas with CT attenuation values below -950 HU.
FAU - Irion, Klaus L
AU  - Irion KL
AD  - Liverpool Heart and Chest Hospital NHS Trust, Royal Liverpool University 
      Hospital, Liverpool, United Kingdom. Klaus.irion@LHCH.NHS.UK
FAU - Hocchegger, Bruno
AU  - Hocchegger B
FAU - Marchiori, Edson
AU  - Marchiori E
FAU - Holemans, John A
AU  - Holemans JA
FAU - Smith, Rupert A
AU  - Smith RA
FAU - Raja, Ramesh C
AU  - Raja RC
FAU - Singanayagam, Selvadurai
AU  - Singanayagam S
LA  - eng
PT  - Case Reports
PT  - Journal Article
PL  - United States
TA  - J Thorac Imaging
JT  - Journal of thoracic imaging
JID - 8606160
SB  - IM
MH  - Child
MH  - Female
MH  - Humans
MH  - Lung Diseases/*diagnostic imaging
MH  - Proteus Syndrome/*diagnostic imaging
MH  - Radiographic Image Interpretation, Computer-Assisted
MH  - Radiography, Thoracic
MH  - Tomography, X-Ray Computed/*methods
EDAT- 2009/02/27 09:00
MHDA- 2009/06/17 09:00
CRDT- 2009/02/27 09:00
PHST- 2009/02/27 09:00 [entrez]
PHST- 2009/02/27 09:00 [pubmed]
PHST- 2009/06/17 09:00 [medline]
AID - 00005382-200902000-00011 [pii]
AID - 10.1097/RTI.0b013e31818b20cd [doi]
PST - ppublish
SO  - J Thorac Imaging. 2009 Feb;24(1):45-8. doi: 10.1097/RTI.0b013e31818b20cd.