PMID- 20430517 OWN - NLM STAT- MEDLINE DCOM- 20100908 LR - 20100607 IS - 1872-6968 (Electronic) IS - 0303-8467 (Linking) VI - 112 IP - 6 DP - 2010 Jul TI - Sporadic Creutzfeldt-Jakob disease presenting as nonconvulsive status epilepticus case report and review of the literature. PG - 537-40 LID - 10.1016/j.clineuro.2010.03.025 [doi] AB - Creutzfeldt-Jakob disease (CJD) is the most common transmissible human spongiform encephalopathy. Seizures and status epilepticus (SE) are an uncommon finding in CJD. We report a 64-year-old woman with rapid cognitive decline who had electroencephalographic (EEG) changes suggestive of nonconvulsive status epilepticus (NCSE). She was later diagnosed with sporadic CJD (sCJD). We also reviewed the literature for published cases on this topic. MEDLINE was employed to identify all published reports of CJD and SE. We identified 8 references with a total of 12 cases with CJD and NCSE. sCJD should be considered in the differential diagnosis of any patient who presents with rapid cognitive decline and EEG changes consistent with status epilepticus. CI - Copyright 2010 Elsevier B.V. All rights reserved. FAU - Espinosa, Patricio S AU - Espinosa PS AD - Department of Neurology, University of Kentucky College of Medicine, Lexington, KY 40536-0284, USA. ps.espinosa@cien-ecuador.org FAU - Bensalem-Owen, Meriem K AU - Bensalem-Owen MK FAU - Fee, Dominic B AU - Fee DB LA - eng PT - Case Reports PT - Journal Article PT - Review DEP - 20100428 PL - Netherlands TA - Clin Neurol Neurosurg JT - Clinical neurology and neurosurgery JID - 7502039 SB - IM MH - Adult MH - Aged MH - Anxiety Disorders/etiology/psychology MH - Creutzfeldt-Jakob Syndrome/*complications/psychology MH - Electroencephalography MH - Female MH - Humans MH - Hypertension/etiology MH - Magnetic Resonance Imaging MH - Male MH - Middle Aged MH - Status Epilepticus/*etiology MH - Urinary Tract Infections/complications RF - 20 EDAT- 2010/05/01 06:00 MHDA- 2010/09/09 06:00 CRDT- 2010/05/01 06:00 PHST- 2009/06/25 00:00 [received] PHST- 2010/03/26 00:00 [revised] PHST- 2010/03/29 00:00 [accepted] PHST- 2010/05/01 06:00 [entrez] PHST- 2010/05/01 06:00 [pubmed] PHST- 2010/09/09 06:00 [medline] AID - S0303-8467(10)00098-3 [pii] AID - 10.1016/j.clineuro.2010.03.025 [doi] PST - ppublish SO - Clin Neurol Neurosurg. 2010 Jul;112(6):537-40. doi: 10.1016/j.clineuro.2010.03.025. Epub 2010 Apr 28.