PMID- 24327495 OWN - NLM STAT- MEDLINE DCOM- 20140919 LR - 20240109 IS - 2150-136X (Electronic) IS - 2150-1351 (Linking) VI - 4 IP - 3 DP - 2013 Jul TI - Morphology, surgical techniques, and outcomes in patients above 15 years undergoing surgery for congenitally corrected transposition of great arteries. PG - 271-7 LID - 10.1177/2150135113476717 [doi] AB - BACKGROUND: There is a paucity of data about morphology, surgical procedure, and results in older patients with congenitally corrected transposition of great arteries (ccTGAs). PATIENTS AND METHODS: Between January 2002 and August 2012, 15 patients (7 males), median age 25 years, range 16 to 41 years underwent surgery for ccTGA. Associated lesions were tricuspid regurgitation (TR; n = 5) and ventricular septal defect (VSD) with pulmonary stenosis (PS; n = 10). Surgical procedures included tricuspid valve replacement (n = 4), tricuspid valve repair (n = 1), lateral tunnel Fontan (n = 2), extracardiac Fontan (n = 2), Kawashima procedure (n = 1), bidirectional (BD) Glenn (n = 2), Senning + Rastelli procedure (n = 1), and VSD closure + left ventricle to pulmonary artery conduit (n = 1). The details of these procedures and outcomes were analyzed. RESULTS: There were no early or late deaths. Mean follow-up period was 49.9 +/- 26 months. All patients who underwent tricuspid valve replacement are in New York Heart Association (NYHA) class I, with no progression of right ventricular (RV) dysfunction. One patient who underwent tricuspid valve repair is in NYHA class III and has progressed to severe RV dysfunction. None of the patients undergoing single ventricle palliation had any complications related to the surgery. Both patients who underwent anatomical and physiological biventricular (BV) repair had no complications. CONCLUSIONS: Older patients with ccTGA present a challenge. Fontan/BD Glenn remains a good option for patients who presented with VSD PS. Both anatomic and physiological BV repairs provide acceptable results. Tricuspid valve replacement is safe for patients presenting with TR who have improvement in functional class, though the right ventricular function may not improve. FAU - Talwar, Sachin AU - Talwar S AD - Cardiothoracic Centre, All India Institute of Medical Sciences, New Delhi, India. FAU - Ahmed, Tammem AU - Ahmed T FAU - Saxena, Anita AU - Saxena A FAU - Kothari, Shyam Sunder AU - Kothari SS FAU - Juneja, Rajnish AU - Juneja R FAU - Airan, Balram AU - Airan B LA - eng PT - Journal Article PL - United States TA - World J Pediatr Congenit Heart Surg JT - World journal for pediatric & congenital heart surgery JID - 101518415 SB - IM MH - Adolescent MH - Adult MH - Arrhythmias, Cardiac/surgery MH - Cardiac Surgical Procedures/*statistics & numerical data MH - Congenitally Corrected Transposition of the Great Arteries MH - Female MH - Follow-Up Studies MH - Heart Septal Defects/complications/surgery MH - Humans MH - Male MH - Pulmonary Valve Stenosis/complications/surgery MH - Transposition of Great Vessels/complications/pathology/*surgery MH - Treatment Outcome MH - Tricuspid Valve Insufficiency/complications/surgery MH - Young Adult OTO - NOTNLM OT - bidirectional Glenn (BD Glenn) OT - congenitally corrected transposition of great arteries (ccTGA) OT - tricuspid valve repair OT - tricuspid valve replacement (TVR) EDAT- 2013/12/12 06:00 MHDA- 2014/09/23 06:00 CRDT- 2013/12/12 06:00 PHST- 2013/12/12 06:00 [entrez] PHST- 2013/12/12 06:00 [pubmed] PHST- 2014/09/23 06:00 [medline] AID - 4/3/271 [pii] AID - 10.1177/2150135113476717 [doi] PST - ppublish SO - World J Pediatr Congenit Heart Surg. 2013 Jul;4(3):271-7. doi: 10.1177/2150135113476717.