PMID- 25160016 OWN - NLM STAT- MEDLINE DCOM- 20150930 LR - 20140827 IS - 1536-7355 (Electronic) IS - 1076-1608 (Linking) VI - 20 IP - 6 DP - 2014 Sep TI - Bowel-associated dermatosis-arthritis syndrome in an adolescent with short bowel syndrome. PG - 322-4 LID - 10.1097/RHU.0000000000000137 [doi] AB - Bowel-associated dermatosis-arthritis syndrome (BADAS) is a neutrophilic dermatosis, characterized by the occurrence of arthritis and skin lesions related to bowel disease with or without bowel bypass. We report an unusual case of BADAS in a 15-year-old white male with congenital aganglionosis of the colon and hypoganglionosis of the small intestine and multiple bowel surgeries in childhood complicated by short bowel syndrome. He presented with recurrent peripheral polyarthritis, tenosynovitis, and painful erythematous subcutaneous nodules located on the dorsolateral regions of the legs and on the dorsa of the feet. Histological examination disclosed a neutrophilic dermatosis confirming the diagnosis of BADAS.Although an uncommon disease, especially at pediatric age, it is important to evoke the diagnosis of BADAS in children and adolescents with bowel disease, because treatment options and prognosis are distinct from other rheumatologic conditions. FAU - Pereira, Ester AU - Pereira E AD - From the *Hospital Pediatrico de Coimbra and daggerDepartment of Dermatology, Centro Hospitalar e Universitario de Coimbra, EPE, Coimbra, Portugal. FAU - Estanqueiro, Paula AU - Estanqueiro P FAU - Almeida, Susana AU - Almeida S FAU - Ferreira, Ricardo AU - Ferreira R FAU - Tellechea, Oscar AU - Tellechea O FAU - Salgado, Manuel AU - Salgado M LA - eng PT - Case Reports PT - Journal Article PL - United States TA - J Clin Rheumatol JT - Journal of clinical rheumatology : practical reports on rheumatic & musculoskeletal diseases JID - 9518034 RN - 0 (Adrenal Cortex Hormones) RN - 0 (Anti-Bacterial Agents) RN - 0 (Anti-Inflammatory Agents, Non-Steroidal) SB - IM MH - Adolescent MH - Adrenal Cortex Hormones/therapeutic use MH - Anti-Bacterial Agents/therapeutic use MH - Anti-Inflammatory Agents, Non-Steroidal/therapeutic use MH - Arthritis/*diagnosis/drug therapy/epidemiology MH - Comorbidity MH - Hirschsprung Disease/*diagnosis/drug therapy/epidemiology MH - Humans MH - Male MH - Short Bowel Syndrome/*diagnosis/drug therapy/epidemiology MH - Skin Diseases/*diagnosis/drug therapy/epidemiology MH - Tenosynovitis/*diagnosis/drug therapy/epidemiology MH - Treatment Outcome EDAT- 2014/08/28 06:00 MHDA- 2015/10/01 06:00 CRDT- 2014/08/28 06:00 PHST- 2014/08/28 06:00 [entrez] PHST- 2014/08/28 06:00 [pubmed] PHST- 2015/10/01 06:00 [medline] AID - 00124743-201409000-00006 [pii] AID - 10.1097/RHU.0000000000000137 [doi] PST - ppublish SO - J Clin Rheumatol. 2014 Sep;20(6):322-4. doi: 10.1097/RHU.0000000000000137.