PMID- 25386293 OWN - NLM STAT- PubMed-not-MEDLINE DCOM- 20141111 LR - 20200930 IS - 2036-7392 (Print) IS - 2036-7406 (Electronic) IS - 2036-7392 (Linking) VI - 3 IP - 3 DP - 2011 Oct 5 TI - Hyperimmunoglobulin E syndrome in two siblings. PG - e41 LID - 10.4081/dr.2011.e41 [doi] LID - e41 AB - Hyperimmunoglobulin E recurrent infection syndrome (HIES) is characterized by recurrent skin and lung infections, eczema, elevated serum immunoglobulin E (IgE) levels (>2000 IU/mL), various connective tissue, skeletal, and vascular abnormalities.(1) We describe herein two brothers with HIES and documented the complications and management of such involvement. FAU - Hawilo, Abdulmohti AU - Hawilo A AD - Dermatology Department, La Rabta Hospital, Faculte de Medecine, Universite El Manar, Tunis, Tunisia. FAU - Zaraa, Ines AU - Zaraa I AD - Dermatology Department, La Rabta Hospital, Faculte de Medecine, Universite El Manar, Tunis, Tunisia. FAU - Trojjet, Sondes AU - Trojjet S AD - Dermatology Department, La Rabta Hospital, Faculte de Medecine, Universite El Manar, Tunis, Tunisia. FAU - Zribi, Hella AU - Zribi H AD - Dermatology Department, La Rabta Hospital, Faculte de Medecine, Universite El Manar, Tunis, Tunisia. FAU - Rouhou, Rym Cheikh AU - Rouhou RC AD - Dermatology Department, La Rabta Hospital, Faculte de Medecine, Universite El Manar, Tunis, Tunisia. FAU - Euch, Dalenda El AU - Euch DE AD - Dermatology Department, La Rabta Hospital, Faculte de Medecine, Universite El Manar, Tunis, Tunisia. FAU - Mokni, Mourad AU - Mokni M AD - Dermatology Department, La Rabta Hospital, Faculte de Medecine, Universite El Manar, Tunis, Tunisia. FAU - Osman, Amel Ben AU - Osman AB AD - Dermatology Department, La Rabta Hospital, Faculte de Medecine, Universite El Manar, Tunis, Tunisia. LA - eng PT - Case Reports DEP - 20111128 PL - Italy TA - Dermatol Reports JT - Dermatology reports JID - 101566470 PMC - PMC4211509 OTO - NOTNLM OT - atopic dermatitis OT - hyper-IgE syndrome OT - infection. OT - primary immunodeficiency EDAT- 2011/10/05 00:00 MHDA- 2011/10/05 00:01 PMCR- 2011/11/28 CRDT- 2014/11/12 06:00 PHST- 2011/07/20 00:00 [received] PHST- 2011/09/12 00:00 [accepted] PHST- 2014/11/12 06:00 [entrez] PHST- 2011/10/05 00:00 [pubmed] PHST- 2011/10/05 00:01 [medline] PHST- 2011/11/28 00:00 [pmc-release] AID - dr.2011.e41 [pii] AID - 10.4081/dr.2011.e41 [doi] PST - epublish SO - Dermatol Reports. 2011 Nov 28;3(3):e41. doi: 10.4081/dr.2011.e41. eCollection 2011 Oct 5.