PMID- 26120576 OWN - NLM STAT- PubMed-not-MEDLINE DCOM- 20150629 LR - 20201001 IS - 2296-9705 (Print) IS - 2296-9705 (Electronic) VI - 5 IP - 2 DP - 2015 May-Aug TI - ANCA-Associated Vasculitis in a Patient with Systematic Sclerosis and Sjogren's Syndrome: A Case Report. PG - 113-7 LID - 10.1159/000381946 [doi] AB - A 65-year-old woman with a limited form of systematic sclerosis (SSc) and Sjogren's syndrome (SS) was admitted to our hospital for the evaluation of renal dysfunction. Her serum creatinine was 1.6 mg/dl, proteinuria was 1.6 g/day, and the urine sediment contained 20-29 erythrocytes/high-power field. Myeloperoxidase anti-neutrophil cytoplasmic antibodies, anti-SS-A/SS-B antibodies and anti-centromere antibodies were positive. A renal biopsy showed focal necrotizing glomerulonephritis with focal interstitial lymphoplasmacytic infiltration. A diagnosis of anti-neutrophil cytoplasmic antibody-associated vasculitis (AAV) was made. A steroid therapy was initiated and AAV subsided. This is a rare case of AAV in a patient with anti-centromere-positive limited SSc and SS. FAU - Kubota, Keiichi AU - Kubota K AD - Nephrology Center, Toranomon Hospital, Tokyo, Japan. FAU - Ueno, Toshiharu AU - Ueno T AD - Nephrology Center, Toranomon Hospital, Tokyo, Japan. FAU - Mise, Koki AU - Mise K AD - Nephrology Center, Toranomon Hospital, Tokyo, Japan. FAU - Hazue, Ryo AU - Hazue R AD - Nephrology Center, Toranomon Hospital, Tokyo, Japan. FAU - Suwabe, Tatsuya AU - Suwabe T AD - Nephrology Center, Toranomon Hospital, Tokyo, Japan. FAU - Kikuchi, Koichi AU - Kikuchi K AD - Nephrology Center, Toranomon Hospital, Tokyo, Japan. FAU - Hoshino, Junichi AU - Hoshino J AD - Nephrology Center, Toranomon Hospital, Tokyo, Japan. FAU - Sumida, Keiichi AU - Sumida K AD - Nephrology Center, Toranomon Hospital, Tokyo, Japan. FAU - Hayami, Noriko AU - Hayami N AD - Nephrology Center, Toranomon Hospital, Tokyo, Japan. FAU - Takaichi, Kenmei AU - Takaichi K AD - Nephrology Center, Toranomon Hospital, Tokyo, Japan ; Okinaka Memorial Institute for Medical Research, Tokyo, Japan. FAU - Fujii, Takeshi AU - Fujii T AD - Department of Pathology, Toranomon Hospital, Tokyo, Japan. FAU - Ohashi, Kenichi AU - Ohashi K AD - Department of Pathology, Toranomon Hospital, Tokyo, Japan. FAU - Nonomura, Yoshinori AU - Nonomura Y AD - Department of Rheumatology, Tokyo Kyosai Hospital, Tokyo, Japan. FAU - Ubara, Yosifumi AU - Ubara Y AD - Nephrology Center, Toranomon Hospital, Tokyo, Japan ; Okinaka Memorial Institute for Medical Research, Tokyo, Japan. LA - eng PT - Case Reports DEP - 20150505 PL - Switzerland TA - Case Rep Nephrol Dial JT - Case reports in nephrology and dialysis JID - 101636294 PMC - PMC4464031 OTO - NOTNLM OT - ANCA-associated vasculitis OT - Anti-neutrophil cytoplasmic antibody OT - Sjogren's syndrome OT - Systemic sclerosis EDAT- 2015/06/30 06:00 MHDA- 2015/06/30 06:01 PMCR- 2015/05/05 CRDT- 2015/06/30 06:00 PHST- 2015/06/30 06:00 [entrez] PHST- 2015/06/30 06:00 [pubmed] PHST- 2015/06/30 06:01 [medline] PHST- 2015/05/05 00:00 [pmc-release] AID - cnd-0005-0113 [pii] AID - 10.1159/000381946 [doi] PST - epublish SO - Case Rep Nephrol Dial. 2015 May 5;5(2):113-7. doi: 10.1159/000381946. eCollection 2015 May-Aug.