PMID- 26426189
OWN - NLM
STAT- PubMed-not-MEDLINE
LR  - 20191120
IS  - 0043-3144 (Print)
IS  - 2309-5830 (Electronic)
IS  - 0043-3144 (Linking)
VI  - 64
IP  - 3
DP  - 2015 Jun
TI  - Tricuspid Atresia 18 Years Post Glenn: Is Fontan Necessary in All Cases?
PG  - 294-7
LID - 10.7727/wimj.2014.272 [doi]
AB  - Tricuspid atresia is a rare cyanotic congenital heart disease, first described by 
      Kreysig (1817), has an incidence of 1% to 5%. It is incompatible with longevity 
      without surgical intervention. Glenn (1958) was successful in using a superior 
      vena cava to right pulmonary artery anastomosis. Fontan (1958) was successful in 
      separating the right and left cardiac circulation; this is the surgical method of 
      choice, with death of 17% by 20 years of age. The Fontan circulation has burdens 
      of multisystem abnormalities, including ventricular dysfunction (72%), 
      dysrhythmias (40%) and renal, hepatic, gastrointestinal and pulmonary 
      complications. The index case is the oldest documented report of tricuspid 
      atresia with rudimentary right ventricle and concordant ventriculo-arterial 
      connections, 18 years post Glen only, from two years of age. She is asymptomatic, 
      of high intellect, never used medications and is now functioning at New York 
      Heart Association (NYHA) I-II, at 20 years of age. Her survival and function was 
      secondary to an innate large atrial and ventricular communication with normal 
      left ventricle, mitral, aortic and pulmonary valves, indicating Fontan may not be 
      needed in all structural anatomic cases of tricuspid atresia.
FAU - Williams-Phillips, S
AU  - Williams-Phillips S
AD  - Andrews Memorial Hospital, TAI Wing, 27 Hope Road, Kingston 10, Jamaica. 
      sandrap@cwjamaica.com.
LA  - eng
PT  - Journal Article
DEP - 20150505
PL  - Jamaica
TA  - West Indian Med J
JT  - The West Indian medical journal
JID - 0417410
SB  - IM
PMC - PMC4763911
EDAT- 2015/10/02 06:00
MHDA- 2015/10/02 06:01
PMCR- 2016/06/01
CRDT- 2015/10/02 06:00
PHST- 2014/10/15 00:00 [received]
PHST- 2014/10/31 00:00 [accepted]
PHST- 2015/10/02 06:00 [entrez]
PHST- 2015/10/02 06:00 [pubmed]
PHST- 2015/10/02 06:01 [medline]
PHST- 2016/06/01 00:00 [pmc-release]
AID - wimj.2014.272 [pii]
AID - 10.7727/wimj.2014.272 [doi]
PST - ppublish
SO  - West Indian Med J. 2015 Jun;64(3):294-7. doi: 10.7727/wimj.2014.272. Epub 2015 
      May 5.