PMID- 27035001
OWN - NLM
STAT- MEDLINE
DCOM- 20160421
LR  - 20181023
IS  - 0040-3660 (Print)
IS  - 0040-3660 (Linking)
VI  - 87
IP  - 12
DP  - 2015
TI  - [Multiple endocrine neoplasia type 1 syndrome with three classical components and 
      chiasm glioma: specific features of target organ lesions and a clinical 
      observation].
PG  - 122-127
LID - 10.17116/terarkh20158712122-127 [doi]
AB  - The article briefly reviews the specific features of target-organ lesions in 
      multiple endocrine neoplasia type 1 (MEN1) syndrome and a clinical case of 
      genetically confirmed MEN1 syndrome in a young female patient. Despite the 
      relative rarity of this disease, timely diagnosis, treatment and screening for 
      its main components are very important for the overall prognosis of patients with 
      MEN1 and their first-degree relatives who are MEN1 gene mutation carriers. The 
      described case is noteworthy for a number of specific features. The authors could 
      find no account of optic chiasm glioma within the framework of MEN1 in the 
      literature. Moreover, therapy-resistant somatoprolactinoma engages attention, 
      which points to its aggressive nature with pituitary adenoma that is not been 
      clearly visualized on magnetic resonance imaging. Of interest is the order of 
      detection of neoplasms, in particular the manifestation of hypoglycemic episodes 
      as a sign of organic hyperinsulinism. which have been initially regarded as 
      epileptic seizures, after the use of sustained-release somatostatin analogues for 
      the treatment of acromegaly.
FAU - Mokrysheva, N G
AU  - Mokrysheva NG
AD  - Endocrinology Research Center, Ministry of Health of Russia, Moscow, Russia.
FAU - Mamedova, E O
AU  - Mamedova EO
AD  - Endocrinology Research Center, Ministry of Health of Russia, Moscow, Russia.
FAU - Pigarova, E A
AU  - Pigarova EA
AD  - Endocrinology Research Center, Ministry of Health of Russia, Moscow, Russia.
FAU - Berezkina, Yu A
AU  - Berezkina YA
AD  - Endocrinology Research Center, Ministry of Health of Russia, Moscow, Russia.
FAU - Vorontsov, A V
AU  - Vorontsov AV
AD  - Endocrinology Research Center, Ministry of Health of Russia, Moscow, Russia.
FAU - Azizyan, V N
AU  - Azizyan VN
AD  - Endocrinology Research Center, Ministry of Health of Russia, Moscow, Russia.
FAU - Grigoriev, A Yu
AU  - Grigoriev AY
AD  - Endocrinology Research Center, Ministry of Health of Russia, Moscow, Russia.
FAU - Alekseeva, T R
AU  - Alekseeva TR
AD  - N.N. Blokhin Russian Cancer Research Center, Moscow, Russia.
FAU - Kutin, M A
AU  - Kutin MA
AD  - Acad. N.N. Burdenko Research Institute of Neurosurgery, Moscow, Russia.
FAU - Kochatkov, A V
AU  - Kochatkov AV
AD  - A.V. Vishnevsky Institute of Surgery, Ministry of Health of Russia, Moscow, 
      Russia.
FAU - Rozhinskaya, L Ya
AU  - Rozhinskaya LY
AD  - Endocrinology Research Center, Ministry of Health of Russia, Moscow, Russia.
LA  - rus
PT  - Case Reports
PT  - English Abstract
PT  - Journal Article
PT  - Review
PL  - Russia (Federation)
TA  - Ter Arkh
JT  - Terapevticheskii arkhiv
JID - 2984818R
SB  - IM
MH  - Adult
MH  - Female
MH  - Glioma/etiology/*pathology
MH  - Humans
MH  - Multiple Endocrine Neoplasia Type 1/*complications
MH  - Optic Chiasm/*pathology
MH  - Optic Nerve Neoplasms/etiology/*pathology
EDAT- 2015/01/01 00:00
MHDA- 2016/04/22 06:00
CRDT- 2016/04/02 06:00
PHST- 2016/04/02 06:00 [entrez]
PHST- 2015/01/01 00:00 [pubmed]
PHST- 2016/04/22 06:00 [medline]
AID - 10.17116/terarkh20158712122-127 [doi]
PST - ppublish
SO  - Ter Arkh. 2015;87(12):122-127. doi: 10.17116/terarkh20158712122-127.