PMID- 28431954 OWN - NLM STAT- MEDLINE DCOM- 20180319 LR - 20181202 IS - 1532-2653 (Electronic) IS - 0967-5868 (Linking) VI - 43 DP - 2017 Sep TI - Isolated intracranial fibromuscular dysplasia of the posterior cerebral artery. PG - 119-121 LID - S0967-5868(17)30105-4 [pii] LID - 10.1016/j.jocn.2017.04.003 [doi] AB - Fibromuscular dysplasia (FMD) is a nonatherosclerotic, noninflammatory arterial disease that most commonly affects the renal and internal carotid arteries, but intracranial FMD is very rare. We report a patient with FMD involving the posterior cerebral arteries (PCAs). A 24year old female was presented with a 4day history of right homonymous hemianopsia with throbbing headache in the left temporo-occipital area. The brain magnetic resonance imaging (MRI) revealed an acute ischemic stroke in the left PCA territory, while the Time of Flight (TOF) magnetic resonance angiogram (MRA) showed segmental luminal irregularities in the left proximal PCA. The conventional angiogram revealed the "string of beads" appearance, a characteristic that is pathognomonic for FMD. The patient's inhospital clinical course was stable, while there was no recurrence of stroke. This is the second report of FMD of the PCA. Notwithstanding incredibly rare incidences of isolated intracranial FMD and nonspecific findings of MRA, such a pathophysiology should be considered as the cause for a stroke in young patients, especially those with no cardiovascular risk factor. CI - Copyright (c) 2017 Elsevier Ltd. All rights reserved. FAU - Yeo, Min-Ju AU - Yeo MJ AD - Department of Neurology, Chungbuk National University Hospital, Cheongju, Republic of Korea. FAU - Jeon, Ho-Yeong AU - Jeon HY AD - Department of Neurology, Chungbuk National University Hospital, Cheongju, Republic of Korea. FAU - Cha, Min-Ju AU - Cha MJ AD - Department of Neurology, Chungbuk National University Hospital, Cheongju, Republic of Korea. FAU - Jang, Hye-Yeon AU - Jang HY AD - Department of Neurology, Chungbuk National University Hospital, Cheongju, Republic of Korea. FAU - Lee, Sang-Gil AU - Lee SG AD - Department of Neurology, Chungbuk National University Hospital, Cheongju, Republic of Korea. FAU - Seon Kim, Ji AU - Seon Kim J AD - Department of Neurology, Chungbuk National University Hospital, Cheongju, Republic of Korea. FAU - Lee, Sung-Hyun AU - Lee SH AD - Department of Neurology, Chungbuk National University Hospital, Cheongju, Republic of Korea. FAU - Lee, Sang-Soo AU - Lee SS AD - Department of Neurology, Chungbuk National University Hospital, Cheongju, Republic of Korea. FAU - Shin, Dong-Ick AU - Shin DI AD - Department of Neurology, Chungbuk National University Hospital, Cheongju, Republic of Korea. Electronic address: mdmju@naver.com. LA - eng PT - Case Reports PT - Journal Article DEP - 20170418 PL - Scotland TA - J Clin Neurosci JT - Journal of clinical neuroscience : official journal of the Neurosurgical Society of Australasia JID - 9433352 SB - IM MH - Female MH - *Fibromuscular Dysplasia/complications/diagnosis/diagnostic imaging/pathology MH - Humans MH - Posterior Cerebral Artery/*pathology MH - Stroke/complications/diagnostic imaging MH - Young Adult OTO - NOTNLM OT - Fibromuscular dysplasia OT - Intracranial OT - Posterior cerebral artery EDAT- 2017/04/23 06:00 MHDA- 2018/03/20 06:00 CRDT- 2017/04/23 06:00 PHST- 2017/01/20 00:00 [received] PHST- 2017/04/03 00:00 [accepted] PHST- 2017/04/23 06:00 [pubmed] PHST- 2018/03/20 06:00 [medline] PHST- 2017/04/23 06:00 [entrez] AID - S0967-5868(17)30105-4 [pii] AID - 10.1016/j.jocn.2017.04.003 [doi] PST - ppublish SO - J Clin Neurosci. 2017 Sep;43:119-121. doi: 10.1016/j.jocn.2017.04.003. Epub 2017 Apr 18.