PMID- 28747599
OWN - NLM
STAT- MEDLINE
DCOM- 20171005
LR  - 20171015
IS  - 1349-7413 (Electronic)
IS  - 0911-4300 (Linking)
VI  - 40
IP  - 3
DP  - 2017
TI  - [Interstitial pneumonia with autoimmune features].
PG  - 139-144
LID - 10.2177/jsci.40.139 [doi]
AB  - Some patients with idiopathic interstitial pneumonias (IIPs) have clinical 
      features that suggest autoimmune process but not fulfill established criteria for 
      connective tissue disease (CTD). Different terms and criteria have been proposed 
      to describe these patients, which includes undifferentiated connective tissue 
      disease (UCTD), lung dominant connective tissue disease (LD-CTD), and 
      autoimmune-featured interstitial lung disease (AIF-ILD). To marshal these 
      ununiform classification criteria, the "European Respiratory Society/American 
      Thoracic Society Task Force on Undifferentiated Forms of Connective Tissue 
      Disease-associated Interstitial Lung Disease" proposed a consensus regarding the 
      nomenclature and classification criteria for patients with IIP and features of 
      autoimmunity with the term "interstitial pneumonia with autoimmune features" 
      (IPAF). It was reported that patients with IPAF accounted for 7.3% approximately 34.1% of 
      patients with interstitial lung disease (ILD). Survival, rate of progressing to 
      CTD, appropriate treatment, and treatment response are not yet elucidated. 
      Furthermore, it is not determined whether IPAF is a distinct category of ILD or 
      simply a part of IIP. These questions should be elucidated by future prospective 
      cohort studies. Hopefully, rheumatologists should participate in not only 
      clinical trials but also in multidisciplinary discussions for IPAF.
FAU - Nishiyama, Osamu
AU  - Nishiyama O
AD  - Department of Respiratory Medicine and Allergology, Kindai University, Faculty of 
      Medicine.
FAU - Tohda, Yuji
AU  - Tohda Y
AD  - Department of Respiratory Medicine and Allergology, Kindai University, Faculty of 
      Medicine.
LA  - jpn
PT  - Journal Article
PT  - Review
PL  - Japan
TA  - Nihon Rinsho Meneki Gakkai Kaishi
JT  - Nihon Rinsho Men'eki Gakkai kaishi = Japanese journal of clinical immunology
JID - 9505992
SB  - IM
MH  - *Autoimmunity
MH  - Connective Tissue Diseases/diagnosis/etiology/immunology
MH  - Disease Progression
MH  - Humans
MH  - Lung Diseases, Interstitial/classification/complications/diagnosis/*immunology
OTO - NOTNLM
OT  - autoimmune feature
OT  - connective tissue disease
OT  - idiopathic interstitial pneumonia
OT  - interstitial lung disease
EDAT- 2017/07/28 06:00
MHDA- 2017/10/06 06:00
CRDT- 2017/07/28 06:00
PHST- 2017/07/28 06:00 [entrez]
PHST- 2017/07/28 06:00 [pubmed]
PHST- 2017/10/06 06:00 [medline]
AID - 10.2177/jsci.40.139 [doi]
PST - ppublish
SO  - Nihon Rinsho Meneki Gakkai Kaishi. 2017;40(3):139-144. doi: 10.2177/jsci.40.139.