PMID- 28753703
OWN - NLM
STAT- MEDLINE
DCOM- 20190520
LR  - 20190520
IS  - 1438-8790 (Electronic)
IS  - 0934-8387 (Linking)
VI  - 71
IP  - 9
DP  - 2017 Sep
TI  - [A Rare Cause of a Spontaneous Pneumothorax].
PG  - 590-593
LID - 10.1055/s-0043-112886 [doi]
AB  - A young patient presented himself to the emergency department with sudden-onset, 
      breathing-dependent right-sided thoracic pain. The auscultation revealed 
      diminished breath sounds on the right. The radiograph showed a pneumothorax which 
      was immediately dealt with chest tube drainage. The CT scan of the thorax showed 
      minuscule subpleural bullae. Video-assisted thoracoscopic surgery (VATS) was 
      performed due to persistent fistulae formation through the drain. The subpleural, 
      bullous and emphysematous changes were histologically confirmed. Investigations 
      into the cause showed evidence of alpha-1-antitrypsin deficiency (AATD). The 
      patient is a Pi MZ type. Few cases of spontaneous pneumothorax as the first 
      manifestation of alpha-1-antitrypsin deficiency have been described. Conclusion: 
      When diagnosing primary spontaneous pneumothorax, alpha-1-antitrypsin deficiency 
      should be considered.
CI  - (c) Georg Thieme Verlag KG Stuttgart . New York.
FAU - Lepiorz, M
AU  - Lepiorz M
AD  - Klinik fur Pneumologie und konservative Intensivmedizin - Krankenhaus Barmherzige 
      Bruder, Regensburg.
FAU - Grosser, C
AU  - Grosser C
AD  - Klinik fur Thoraxchirurgie - Krankenhaus Barmherzige Bruder, Regensburg.
FAU - Hofmann, H-S
AU  - Hofmann HS
AD  - Klinik fur Thoraxchirurgie - Krankenhaus Barmherzige Bruder, Regensburg.
FAU - Pfeifer, M
AU  - Pfeifer M
AD  - Klinik fur Pneumologie und konservative Intensivmedizin - Krankenhaus Barmherzige 
      Bruder, Regensburg.
LA  - ger
PT  - Case Reports
PT  - Journal Article
TT  - Seltene Ursache eines Spontanpneumothorax.
DEP - 20170728
PL  - Germany
TA  - Pneumologie
JT  - Pneumologie (Stuttgart, Germany)
JID - 8906641
SB  - IM
MH  - Diagnosis, Differential
MH  - Drainage
MH  - Follow-Up Studies
MH  - Humans
MH  - Lung/pathology
MH  - Male
MH  - Pneumonectomy
MH  - Pneumothorax/diagnosis/*etiology/pathology/surgery
MH  - Pulmonary Emphysema/*diagnosis/pathology/surgery
MH  - Thoracoscopy
MH  - Tomography, X-Ray Computed
MH  - Young Adult
MH  - alpha 1-Antitrypsin Deficiency/*diagnosis/pathology/surgery
COIS- Interessenkonflikt: Die Autoren geben an, dass kein Interessenskonflikt besteht.
EDAT- 2017/07/29 06:00
MHDA- 2019/05/21 06:00
CRDT- 2017/07/29 06:00
PHST- 2017/07/29 06:00 [pubmed]
PHST- 2019/05/21 06:00 [medline]
PHST- 2017/07/29 06:00 [entrez]
AID - 10.1055/s-0043-112886 [doi]
PST - ppublish
SO  - Pneumologie. 2017 Sep;71(9):590-593. doi: 10.1055/s-0043-112886. Epub 2017 Jul 
      28.