PMID- 28961825
OWN - NLM
STAT- MEDLINE
DCOM- 20180529
LR  - 20220408
IS  - 1569-8041 (Electronic)
IS  - 0923-7534 (Print)
IS  - 0923-7534 (Linking)
VI  - 28
IP  - 10
DP  - 2017 Oct 1
TI  - An update on the management of sporadic desmoid-type fibromatosis: a European 
      Consensus Initiative between Sarcoma PAtients EuroNet (SPAEN) and European 
      Organization for Research and Treatment of Cancer (EORTC)/Soft Tissue and Bone 
      Sarcoma Group (STBSG).
PG  - 2399-2408
LID - S0923-7534(19)34935-X [pii]
LID - 10.1093/annonc/mdx323 [doi]
AB  - Desmoid-type fibromatosis is a rare and locally aggressive monoclonal, 
      fibroblastic proliferation characterized by a variable and often unpredictable 
      clinical course. Currently, there is no established or evidence-based treatment 
      approach available for this disease. Therefore, in 2015 the European Desmoid 
      Working Group published a position paper giving recommendations on the treatment 
      of this intriguing disease. Here, we present an update of this consensus approach 
      based on professionals' AND patients' expertise following a round table meeting 
      bringing together sarcoma experts from the European Organization for Research and 
      Treatment of Cancer/Soft Tissue and Bone Sarcoma Group with patients and patient 
      advocates from Sarcoma PAtients EuroNet. In this paper, we focus on new findings 
      regarding the prognostic value of mutational analysis in desmoid-type 
      fibromatosis patients and new systemic treatment options.
CI  - (c) The Author 2017. Published by Oxford University Press on behalf of the European 
      Society for Medical Oncology.
FAU - Kasper, B
AU  - Kasper B
AD  - Sarcoma Unit, Interdisciplinary Tumor Center, Mannheim University Medical Center, 
      University of Heidelberg, Mannheim;. Electronic address: bernd.kasper@umm.de.
FAU - Baumgarten, C
AU  - Baumgarten C
AD  - SPAEN Sarcoma PAtients EuroNet e.V, Wolfersheim, Germany.
FAU - Garcia, J
AU  - Garcia J
AD  - SPAEN Sarcoma PAtients EuroNet e.V, Wolfersheim, Germany.
FAU - Bonvalot, S
AU  - Bonvalot S
AD  - Department of Surgical Oncology, Institut Curie, PSL University, Paris, France.
FAU - Haas, R
AU  - Haas R
AD  - Department of Radiotherapy, The Netherlands Cancer Institute-Antoni van 
      Leeuwenhoek Hospital, Amsterdam;; Department of Radiotherapy, Leiden University 
      Medical Center, Leiden, The Netherlands.
FAU - Haller, F
AU  - Haller F
AD  - Institute of Pathology, Friedrich Alexander University Erlangen, Erlangen, 
      Germany.
FAU - Hohenberger, P
AU  - Hohenberger P
AD  - Sarcoma Unit, Interdisciplinary Tumor Center, Mannheim University Medical Center, 
      University of Heidelberg, Mannheim.
FAU - Penel, N
AU  - Penel N
AD  - Department of Medical Oncology, Centre Oscar Lambret, Lille, France.
FAU - Messiou, C
AU  - Messiou C
AD  - Department of Radiology, The Royal Marsden Hospital, London.
FAU - van der Graaf, W T
AU  - van der Graaf WT
AD  - Division of Clinical Studies, The Institute of Cancer Research, London, UK.
FAU - Gronchi, A
AU  - Gronchi A
AD  - Department of Surgery, Fondazione IRCCS Istituto Nazionale dei Tumori, Milan, 
      Italy. Electronic address: alessandro.gronchi@istitutotumori.mi.it.
CN  - Desmoid Working Group
LA  - eng
PT  - Journal Article
PT  - Practice Guideline
PT  - Review
PL  - England
TA  - Ann Oncol
JT  - Annals of oncology : official journal of the European Society for Medical 
      Oncology
JID - 9007735
SB  - IM
MH  - Fibromatosis, Aggressive/*diagnosis/genetics/*therapy
MH  - Humans
MH  - Randomized Controlled Trials as Topic
PMC - PMC5834048
OTO - NOTNLM
OT  - EORTC/STBSG
OT  - SPAEN
OT  - aggressive fibromatosis
OT  - desmoid
OT  - patient advocacy groups
OT  - treatment algorithm
FIR - Bauer, S
IR  - Bauer S
FIR - Blay, J Y
IR  - Blay JY
FIR - van Coevorden, F
IR  - van Coevorden F
FIR - Dileo, P
IR  - Dileo P
FIR - Durr, H R
IR  - Durr HR
FIR - Fiore, M
IR  - Fiore M
FIR - Grunwald, V
IR  - Grunwald V
FIR - Jones, R
IR  - Jones R
FIR - Judson, I
IR  - Judson I
FIR - Kettelhack, C
IR  - Kettelhack C
FIR - Kopeckova, K
IR  - Kopeckova K
FIR - Lazar, A
IR  - Lazar A
FIR - Lindner, L H
IR  - Lindner LH
FIR - Martin-Broto, J
IR  - Martin-Broto J
FIR - Rutkowski, P
IR  - Rutkowski P
FIR - Stacchiotti, S
IR  - Stacchiotti S
FIR - Stoeckle, E
IR  - Stoeckle E
FIR - Valverde, C
IR  - Valverde C
FIR - Verhoef, K
IR  - Verhoef K
FIR - Wardelmann, E
IR  - Wardelmann E
FIR - Wartenberg, M
IR  - Wartenberg M
EDAT- 2017/09/30 06:00
MHDA- 2018/05/31 06:00
PMCR- 2018/10/01
CRDT- 2017/09/30 06:00
PHST- 2017/09/30 06:00 [entrez]
PHST- 2017/09/30 06:00 [pubmed]
PHST- 2018/05/31 06:00 [medline]
PHST- 2018/10/01 00:00 [pmc-release]
AID - S0923-7534(19)34935-X [pii]
AID - mdx323 [pii]
AID - 10.1093/annonc/mdx323 [doi]
PST - ppublish
SO  - Ann Oncol. 2017 Oct 1;28(10):2399-2408. doi: 10.1093/annonc/mdx323.