PMID- 28994016 OWN - NLM STAT- MEDLINE DCOM- 20180622 LR - 20220408 IS - 1534-6307 (Electronic) IS - 1523-3774 (Linking) VI - 19 IP - 11 DP - 2017 Oct 9 TI - Cardiopulmonary Manifestations of Collagen Vascular Diseases. PG - 71 LID - 10.1007/s11926-017-0697-x [doi] AB - PURPOSE OF REVIEW: The study aimed to illustrate the cardiopulmonary findings of the following collagen vascular diseases on cross-sectional imaging: rheumatoid arthritis, scleroderma (progressive systemic sclerosis), systemic lupus erythematosus, the inflammatory myopathies (polymyositis/dermatomyositis), and Sjogren's syndrome. RECENT FINDINGS: Although collagen vascular diseases can affect any part of the body, interstitial lung disease and pulmonary hypertension are the two most important cardiopulmonary complications and are responsible for the majority of morbidity and mortality in this patient population. Interstitial pneumonia with autoimmune features (IPAF) is a newly described entity that encompasses interstitial lung disease in patients with clinical, serologic, or morphologic features suggestive of but not diagnostic of collagen vascular disease; these patients are thought to have better outcomes than idiopathic interstitial pneumonias. Interstitial lung disease and pulmonary hypertension determine the prognosis in collagen vascular disease patients. IPAF is a new term to label patients with possible collagen vascular disease-related interstitial lung disease. Collagen vascular disease patients are at increased risk for various malignancies. FAU - Jawad, Hamza AU - Jawad H AD - Division of Diagnostic Radiology, Cardiothoracic Imaging Section, Mallinckrodt Institute of Radiology, Washington University in St. Louis, Campus Box 8131, 510 S Kingshighway Blvd, St. Louis, MO, USA. jawadh@wustl.edu. FAU - McWilliams, Sebastian R AU - McWilliams SR AD - Division of Diagnostic Radiology, Cardiothoracic Imaging Section, Mallinckrodt Institute of Radiology, Washington University in St. Louis, Campus Box 8131, 510 S Kingshighway Blvd, St. Louis, MO, USA. FAU - Bhalla, Sanjeev AU - Bhalla S AD - Division of Diagnostic Radiology, Cardiothoracic Imaging Section, Mallinckrodt Institute of Radiology, Washington University in St. Louis, Campus Box 8131, 510 S Kingshighway Blvd, St. Louis, MO, USA. LA - eng PT - Journal Article PT - Review DEP - 20171009 PL - United States TA - Curr Rheumatol Rep JT - Current rheumatology reports JID - 100888970 SB - IM MH - Cardiovascular Diseases/diagnostic imaging/*etiology MH - Connective Tissue Diseases/*complications/diagnostic imaging MH - Heart/*diagnostic imaging MH - Humans MH - Lung/*diagnostic imaging MH - Lung Diseases/diagnostic imaging/*etiology MH - Magnetic Resonance Imaging OTO - NOTNLM OT - Cardiac magnetic resonance imaging OT - Collagen vascular diseases OT - Connective tissue diseases OT - Interstitial lung disease OT - Pulmonary hypertension EDAT- 2017/10/11 06:00 MHDA- 2018/06/23 06:00 CRDT- 2017/10/11 06:00 PHST- 2017/10/11 06:00 [entrez] PHST- 2017/10/11 06:00 [pubmed] PHST- 2018/06/23 06:00 [medline] AID - 10.1007/s11926-017-0697-x [pii] AID - 10.1007/s11926-017-0697-x [doi] PST - epublish SO - Curr Rheumatol Rep. 2017 Oct 9;19(11):71. doi: 10.1007/s11926-017-0697-x.