PMID- 29531383 OWN - NLM STAT- MEDLINE DCOM- 20180605 LR - 20180605 IS - 1827-6806 (Print) IS - 1827-6806 (Linking) VI - 19 IP - 2 DP - 2018 Feb TI - [Kawasaki disease shock syndrome: a case report]. PG - 111-114 LID - 10.1714/2868.28942 [doi] AB - Kawasaki disease is a systemic vasculitis that presents with stable vital signs. Although it is well known that Kawasaki disease can cause myocarditis, tachycardia and heart failure during the acute stage, Kawasaki disease shock syndrome (KDSS) has recently been described. It is characterized by hypotension, signs and symptoms of poor perfusion and a shock-like state. We report the case of a 7-year-old boy with KDSS who presented with persistent fever, conjunctival injection, laterocervical lymphadenitis, and echocardiography showing signs of myocardial dysfunction and shock. The patient's hemodynamic status markedly improved with immunoglobulin therapy. Early recognition of KDSS can be challenging; however, delay in diagnosis may increase the risk of coronary artery abnormalities and death. FAU - Vieni, Giuseppe AU - Vieni G AD - U.O.C. Pediatria e Neonatologia, Ospedale S. Maria delle Croci, AUSL Romagna, Ravenna. FAU - Pusceddu, Sara AU - Pusceddu S AD - U.O.C. Pediatria e Neonatologia, Ospedale S. Maria delle Croci, AUSL Romagna, Ravenna. FAU - Bruno, Ivana AU - Bruno I AD - U.O.C. Pediatria e Neonatologia, Ospedale S. Maria delle Croci, AUSL Romagna, Ravenna. FAU - Ragni, Luca AU - Ragni L AD - U.O. Cardiologia Pediatrica e dell'Eta Evolutiva, Policlinico S. Orsola, Bologna. FAU - Marchetti, Federico AU - Marchetti F AD - U.O.C. Pediatria e Neonatologia, Ospedale S. Maria delle Croci, AUSL Romagna, Ravenna. LA - ita PT - Case Reports PT - Journal Article TT - La "Kawasaki disease shock syndrome": descrizione di un caso clinico. PL - Italy TA - G Ital Cardiol (Rome) JT - Giornale italiano di cardiologia (2006) JID - 101263411 RN - 0 (Immunoglobulins, Intravenous) SB - IM MH - Child MH - Hemodynamics MH - Humans MH - Immunoglobulins, Intravenous/*therapeutic use MH - Male MH - Mucocutaneous Lymph Node Syndrome/*diagnosis/drug therapy/physiopathology MH - Shock/*diagnosis/drug therapy/physiopathology MH - Treatment Outcome EDAT- 2018/03/14 06:00 MHDA- 2018/06/06 06:00 CRDT- 2018/03/14 06:00 PHST- 2018/03/14 06:00 [entrez] PHST- 2018/03/14 06:00 [pubmed] PHST- 2018/06/06 06:00 [medline] AID - 10.1714/2868.28942 [doi] PST - ppublish SO - G Ital Cardiol (Rome). 2018 Feb;19(2):111-114. doi: 10.1714/2868.28942.