PMID- 29772051 OWN - NLM STAT- MEDLINE DCOM- 20190314 LR - 20190314 IS - 2325-8179 (Electronic) IS - 2325-8160 (Linking) VI - 49 IP - 5 DP - 2018 May 1 TI - Optical Coherence Tomography Angiography of Pigmented Paravenous Retinochoroidal Atrophy. PG - 381-383 LID - 10.3928/23258160-20180501-14 [doi] AB - A 58-year-old man with bilateral pigmented paravenous retinochoroidal atrophy (PPRCA) associated with macular coloboma in the right eye underwent color fundus photography and fundus autofluorescence with the California ultra-widefield retinal imaging system (Optos, Dunfermline, UK), spectral-domain optical coherence tomography (SD-OCT) (Heidelberg Spectralis HRA + OCT; Heidelberg Engineering, Heidelberg, Germany), and en face OCT angiography (OCTA) (AngioPlex, Cirrus HD-OCT 5000; Carl Zeiss Meditec, Dublin, CA). The patient presented with a visual acuity of counting fingers in the right eye and 20/32 in the left eye. Fundus examination and SD-OCT showed typical PPRCA alterations in both eyes and a macular coloboma in the right eye. The OCTA showed relative sparing of the retinal capillary plexuses, with diffuse defects in the choriocapillaris. The authors concluded OCTA imaging of PPRCA suggests more insights of the pathogenesis of this disease, showing that the disease primarily affects the choroidal vascular network, with a relative sparing of the retinal vasculature. [Ophthalmic Surg Lasers Imaging Retina. 2018;49:381-383.]. CI - Copyright 2018, SLACK Incorporated. FAU - Cicinelli, Maria Vittoria AU - Cicinelli MV FAU - Giuffre, Chiara AU - Giuffre C FAU - Rabiolo, Alessandro AU - Rabiolo A FAU - Parodi, Maurizio Battaglia AU - Parodi MB FAU - Bandello, Francesco AU - Bandello F LA - eng PT - Case Reports PT - Journal Article PL - United States TA - Ophthalmic Surg Lasers Imaging Retina JT - Ophthalmic surgery, lasers & imaging retina JID - 101599215 RN - Pigmented Paravenous Chorioretinal Atrophy SB - IM MH - Angiography/methods MH - Choroid/blood supply MH - Eye Diseases, Hereditary/*pathology MH - Humans MH - Male MH - Middle Aged MH - Retinal Degeneration/*pathology MH - Retinal Vessels/pathology MH - Tomography, Optical Coherence/*methods EDAT- 2018/05/18 06:00 MHDA- 2019/03/15 06:00 CRDT- 2018/05/18 06:00 PHST- 2017/06/03 00:00 [received] PHST- 2017/11/01 00:00 [accepted] PHST- 2018/05/18 06:00 [entrez] PHST- 2018/05/18 06:00 [pubmed] PHST- 2019/03/15 06:00 [medline] AID - 10.3928/23258160-20180501-14 [doi] PST - ppublish SO - Ophthalmic Surg Lasers Imaging Retina. 2018 May 1;49(5):381-383. doi: 10.3928/23258160-20180501-14.