PMID- 30774002
OWN - NLM
STAT- MEDLINE
DCOM- 20191104
LR  - 20191104
IS  - 0001-5458 (Print)
IS  - 0001-5458 (Linking)
VI  - 119
IP  - 2
DP  - 2019 Apr
TI  - PEComa of the talus: a unique case of a soft tissue tumor within bone.
PG  - 118-122
LID - 10.1080/00015458.2017.1394658 [doi]
AB  - INTRODUCTION: Perivascular epithelioid cell tumor (PEComa) is a family of rare 
      mesenchymal tumors composed of histologically and immunohistochemically 
      distinctive perivascular epithelioid cells (PECs). These tumors have been 
      described at multiple anatomic sites. PEComas presenting in bone are especially 
      rare and they have been reported to be either primary or metastatic lesions. None 
      of them is located at the level of the foot. PATIENT: We report on a case of 
      primary bone PEComa of the talus, the first one to be published to the best of 
      our knowledge. Treatment and result: Limb sparing surgical treatment has been 
      done using intralesional tumor removal, burring and application of argon beam at 
      the tumor walls and primary filling of the tumor cavity by bone cement with so 
      far absence of any tumor recurrence documented by multiple histological sections 
      at second look operation nine months after primary surgery, where cement has been 
      replaced by autologous bone graft, and by subsequent follow-up. CONCLUSIONS: 
      PEComa is a very rare tumor, and its presence in bone is especially rare. The 
      here reported case of PEComa presenting at the level of the talus is, to the best 
      of our knowledge, the first case to be reported in the literature.
FAU - Gebhart, Michael
AU  - Gebhart M
AUID- ORCID: 0000-0003-4299-8895
AD  - a Service de chirurgie orthopedique, de l'Institut Bordet , Universite libre de 
      Bruxelles , Brussels , Belgium.
FAU - Coltofeanu, Andrei
AU  - Coltofeanu A
AD  - b Service de chirurgie orthopedique , Andrei Clinic Hospital, Regina Maria, 
      Medicova , Bucarest , Romania.
LA  - eng
PT  - Case Reports
PT  - Journal Article
DEP - 20190217
PL  - England
TA  - Acta Chir Belg
JT  - Acta chirurgica Belgica
JID - 0370571
SB  - IM
MH  - Bone Neoplasms/diagnostic imaging/pathology/*surgery
MH  - Female
MH  - Humans
MH  - Limb Salvage/*methods
MH  - Middle Aged
MH  - Perivascular Epithelioid Cell Neoplasms/diagnostic imaging/pathology/*surgery
MH  - Talus/diagnostic imaging/pathology/*surgery
OTO - NOTNLM
OT  - PEComa
OT  - bone tumor
OT  - foot tumor
OT  - margin enlarging procedures
OT  - soft tissue tumor
EDAT- 2019/02/19 06:00
MHDA- 2019/11/05 06:00
CRDT- 2019/02/19 06:00
PHST- 2019/02/19 06:00 [pubmed]
PHST- 2019/11/05 06:00 [medline]
PHST- 2019/02/19 06:00 [entrez]
AID - 10.1080/00015458.2017.1394658 [doi]
PST - ppublish
SO  - Acta Chir Belg. 2019 Apr;119(2):118-122. doi: 10.1080/00015458.2017.1394658. Epub 
      2019 Feb 17.