PMID- 31362014 OWN - NLM STAT- MEDLINE DCOM- 20200507 LR - 20200507 IS - 1552-6259 (Electronic) IS - 0003-4975 (Linking) VI - 109 IP - 3 DP - 2020 Mar TI - Venoarterial Extracorporeal Membrane Oxygenation in Sickle Cell Disease for Urgent Cardiac Surgery. PG - e161-e162 LID - S0003-4975(19)31063-X [pii] LID - 10.1016/j.athoracsur.2019.05.093 [doi] AB - Sickle cell disease (SCD) is among the most common genetic diseases, with a recent increase in life expectancy. Patients may therefore need similar surgical procedures as does the general population, including cardiac surgery. Cardiopulmonary bypass is a homeostasis challenge for SCD patients, with high risk of vasoocclusive crisis. In the most severe cases of cardiogenic shock, venoarterial extracorporeal membrane oxygenation (VA-ECMO) may be required, with prolonged exposure to extreme nonphysiological conditions. We report a case of postcardiotomy shock in an SCD patient successfully managed with VA-ECMO. This highlights that SCD should not be a counterindication to VA-ECMO, pending multidisciplinary management. CI - Copyright (c) 2020 The Society of Thoracic Surgeons. Published by Elsevier Inc. All rights reserved. FAU - de Roux, Quentin AU - de Roux Q AD - Service d'Anesthesie-Reanimation Chirurgicale, CHU Henri Mondor, Assistance Publique des Hopitaux de Paris, Creteil, France; U955-IMRB, Equipe 03 "Strategies pharmacologiques et therapeutiques experimentales des insuffisances cardiaques et coronaires," Inserm, UPEC, Ecole Nationale Veterinaire d'Alfort, Maisons-Alfort, France. FAU - Maghrebi, Sami AU - Maghrebi S AD - Service d'Anesthesie-Reanimation Chirurgicale, CHU Henri Mondor, Assistance Publique des Hopitaux de Paris, Creteil, France. FAU - Fiore, Antonio AU - Fiore A AD - Service de Chirurgie Cardiaque, CHU Henri Mondor, Assistance Publique des Hopitaux de Paris, Creteil, France. FAU - Arminot-Fremaux, Margot AU - Arminot-Fremaux M AD - Service d'Anesthesie-Reanimation Chirurgicale, CHU Henri Mondor, Assistance Publique des Hopitaux de Paris, Creteil, France. FAU - Dessalle, Thomas AU - Dessalle T AD - Service d'Anesthesie-Reanimation Chirurgicale, CHU Henri Mondor, Assistance Publique des Hopitaux de Paris, Creteil, France. FAU - Lim, Pascal AU - Lim P AD - Service de Cardiologie, CHU Henri Mondor, Assistance Publique des Hopitaux de Paris, Creteil, France. FAU - Folliguet, Thierry AU - Folliguet T AD - Service de Chirurgie Cardiaque, CHU Henri Mondor, Assistance Publique des Hopitaux de Paris, Creteil, France; Faculte de Medecine, Universite Paris-Est Creteil, Creteil, France. FAU - Bartolucci, Pablo AU - Bartolucci P AD - Faculte de Medecine, Universite Paris-Est Creteil, Creteil, France; Unite des Maladies Genetiques du Globule Rouge, CHU Henri Mondor, Assistance Publique des Hopitaux de Paris, Creteil, France. FAU - Langeron, Olivier AU - Langeron O AD - Service d'Anesthesie-Reanimation Chirurgicale, CHU Henri Mondor, Assistance Publique des Hopitaux de Paris, Creteil, France; Faculte de Medecine, Universite Paris-Est Creteil, Creteil, France. FAU - Mongardon, Nicolas AU - Mongardon N AD - Service d'Anesthesie-Reanimation Chirurgicale, CHU Henri Mondor, Assistance Publique des Hopitaux de Paris, Creteil, France; Faculte de Medecine, Universite Paris-Est Creteil, Creteil, France; U955-IMRB, Equipe 03 "Strategies pharmacologiques et therapeutiques experimentales des insuffisances cardiaques et coronaires," Inserm, UPEC, Ecole Nationale Veterinaire d'Alfort, Maisons-Alfort, France. Electronic address: nicolas.mongardon@aphp.fr. LA - eng PT - Case Reports PT - Journal Article DEP - 20190727 PL - Netherlands TA - Ann Thorac Surg JT - The Annals of thoracic surgery JID - 15030100R SB - IM MH - Adult MH - Anemia, Sickle Cell/complications MH - Cardiac Surgical Procedures MH - *Emergency Treatment MH - Extracorporeal Membrane Oxygenation/*methods MH - Female MH - Femoral Artery MH - Femoral Vein MH - Humans MH - Jugular Veins MH - Postoperative Complications/*therapy MH - Shock/*therapy EDAT- 2019/07/31 06:00 MHDA- 2020/05/08 06:00 CRDT- 2019/07/31 06:00 PHST- 2019/05/12 00:00 [received] PHST- 2019/05/28 00:00 [revised] PHST- 2019/05/30 00:00 [accepted] PHST- 2019/07/31 06:00 [pubmed] PHST- 2020/05/08 06:00 [medline] PHST- 2019/07/31 06:00 [entrez] AID - S0003-4975(19)31063-X [pii] AID - 10.1016/j.athoracsur.2019.05.093 [doi] PST - ppublish SO - Ann Thorac Surg. 2020 Mar;109(3):e161-e162. doi: 10.1016/j.athoracsur.2019.05.093. Epub 2019 Jul 27.