PMID- 31871683 OWN - NLM STAT- PubMed-not-MEDLINE LR - 20231020 IS - 2051-3380 (Print) IS - 2051-3380 (Electronic) IS - 2051-3380 (Linking) VI - 8 IP - 2 DP - 2020 Mar TI - Interstitial pneumonia with autoimmune features that met the proposed diagnostic criteria for IgG4-related respiratory disease. PG - e00512 LID - 10.1002/rcr2.512 [doi] LID - e00512 AB - We held a multidisciplinary discussion (MDD) about a 61-year-old woman who had an interstitial lung disease (ILD) without extrathoracic lesions that met the classification criteria for interstitial pneumonia with autoimmune features (IPAF) and the proposed diagnostic criteria for immunoglobulin G4 (IgG4)-related respiratory disease (IgG4-RRD). Clinically, the marked progression of lung-limited diffuse lesions was consistent with IPAF. Serum IgG4 and rheumatoid factor levels simultaneously increased and did not contribute to a diagnosis. Pathologically, the significant hyperplasia of lymphoid follicles was consistent with rheumatoid arthritis (RA)-associated ILD. Pulmonary venous occlusions by intimal fibrosis and intimal thickening were not important because these occlusions are found in IgG4-related lung disease (IgG4-RLD) and also in IPAF or ILDs related to connective tissue diseases (CTDs). Radiologically, fibrosing shadows that remained in the lung periphery after treatment were compatible with RA-associated chronic ILD. We concluded that the present case was IPAF that met the proposed diagnostic criteria for IgG4-RRD. CI - (c) 2019 The Authors. Respirology Case Reports published by John Wiley & Sons Australia, Ltd on behalf of The Asian Pacific Society of Respirology. FAU - Arakawa, Nobuhito AU - Arakawa N AUID- ORCID: 0000-0002-0937-176X AD - Department of Pulmonary Medicine International University of Health and Welfare Hospital Nasushiobara Japan. FAU - Yamasawa, Hideaki AU - Yamasawa H AD - Department of Pulmonary Medicine International University of Health and Welfare Hospital Nasushiobara Japan. FAU - Takemura, Tamiko AU - Takemura T AD - Department of Pathology Kanagawa Cardiovascular and Respiratory Center Yokohama Japan. FAU - Okada, Shinya AU - Okada S AD - Department of Pathology International University of Health and Welfare Hospital Nasushiobara Japan. FAU - Taki, Takafumi AU - Taki T AD - Department of Chest Surgery International University of Health and Welfare Hospital Nasushiobara Japan. AD - Department of Thoracic Surgery Japan Community Health Care Organization Utsunomiya Hospital Utsunomiya Japan. FAU - Ishikawa, Shigemi AU - Ishikawa S AD - Department of Chest Surgery International University of Health and Welfare Hospital Nasushiobara Japan. LA - eng PT - Case Reports DEP - 20191217 PL - United States TA - Respirol Case Rep JT - Respirology case reports JID - 101631052 PMC - PMC6915050 OTO - NOTNLM OT - Hyperplasia of lymphoid follicles OT - IgG4-related lung disease OT - interstitial pneumonia with autoimmune features OT - multidisciplinary discussion OT - pulmonary venous occlusion EDAT- 2019/12/25 06:00 MHDA- 2019/12/25 06:01 PMCR- 2019/12/17 CRDT- 2019/12/25 06:00 PHST- 2019/07/29 00:00 [received] PHST- 2019/11/24 00:00 [revised] PHST- 2019/11/25 00:00 [accepted] PHST- 2019/12/25 06:00 [entrez] PHST- 2019/12/25 06:00 [pubmed] PHST- 2019/12/25 06:01 [medline] PHST- 2019/12/17 00:00 [pmc-release] AID - RCR2512 [pii] AID - 10.1002/rcr2.512 [doi] PST - epublish SO - Respirol Case Rep. 2019 Dec 17;8(2):e00512. doi: 10.1002/rcr2.512. eCollection 2020 Mar.