PMID- 32076683
OWN - NLM
STAT- PubMed-not-MEDLINE
LR  - 20200928
IS  - 2667-677X (Print)
IS  - 2667-6370 (Electronic)
IS  - 2149-276X (Linking)
VI  - 48
IP  - 1
DP  - 2020 Feb
TI  - Anaesthetic Approach for Patient with Hereditary Angioedema.
PG  - 68-70
LID - 10.5152/TJAR.2019.90522 [doi]
AB  - Hereditary Angioedema (HEA), a disease caused by a mutation in the gene that 
      encodes for the production of the fraction C1 in the complement (C1-INH), is a 
      rare pathology (1/50.000) that causes swelling of the skin and submucosa in 
      various organs, either naturally triggered or provoked by physical and 
      psychological traumas, infections, or by the use of nonsteroidal 
      anti-inflammatory drugs (NSAIDs) and angiotensin-converting enzyme inhibitors 
      (ACEIs). Surgical trauma may spur the HEA crisis, leading to complications such 
      as the swelling of the respiratory tracts and hemodynamic instability. Thus, the 
      pre-surgical approach to HEA patients requires a specific plan that ensures short 
      term prophylaxis, careful intra-operative management, rescue therapy and 
      intensive post-surgery care. We present a report on a video-laparoscopic 
      cholecystectomy approach for a 28-year-old woman diagnosed with asthma and HEA 
      with symptomatic choledocholithiasis. We opted for short-term prophylaxis and 
      immunology with the intravenous application of C1-INH. Ultrasonography imaging 
      showed arterial wall oedema, which could correspond to a manifestation of C1-INH 
      deficiency in the wall of the manipulated arteries during ultrasonography-guided 
      puncture. Once the patient recovered consciousness, she was transferred to the 
      intensive care unit and was discharged on the 6(th) day of hospitalisation.
CI  - (c) Copyright 2020 by Turkish Anaesthesiology and Intensive Care Society.
FAU - Melo, Maize Cordeiro
AU  - Melo MC
AUID- ORCID: 0000-0003-2759-1528
AD  - Hospital of the Clinics of the Federal University of Minas Gerais, Belo 
      Horizonte, Brazil.
FAU - Boas, Walkiria Wingester Vilas
AU  - Boas WWV
AUID- ORCID: 0000-0003-1468-5197
AD  - Hospital of the Clinics of the Federal University of Minas Gerais, Belo 
      Horizonte, Brazil.
FAU - Faria, Marcos Daniel
AU  - Faria MD
AUID- ORCID: 0000-0002-2460-105X
AD  - Hospital of the Clinics of the Federal University of Minas Gerais, Belo 
      Horizonte, Brazil.
FAU - Lima, Alyne Andrade
AU  - Lima AA
AUID- ORCID: 0000-0002-9350-7729
AD  - Hospital of the Clinics of the Federal University of Minas Gerais, Belo 
      Horizonte, Brazil.
FAU - Souza, Rafaela Souto
AU  - Souza RS
AUID- ORCID: 0000-0003-4323-6059
AD  - Hospital of the Clinics of the Federal University of Minas Gerais, Belo 
      Horizonte, Brazil.
LA  - eng
PT  - Case Reports
DEP - 20191111
PL  - Turkey
TA  - Turk J Anaesthesiol Reanim
JT  - Turkish journal of anaesthesiology and reanimation
JID - 101680817
PMC - PMC7001801
OTO - NOTNLM
OT  - Anaesthesia
OT  - C1 complement inhibitory protein
OT  - hereditary angioedema
COIS- Conflict of Interest: The authors have no conflicts of interest to declare.
EDAT- 2020/02/23 06:00
MHDA- 2020/02/23 06:01
PMCR- 2020/02/01
CRDT- 2020/02/21 06:00
PHST- 2018/12/28 00:00 [received]
PHST- 2019/04/21 00:00 [accepted]
PHST- 2020/02/21 06:00 [entrez]
PHST- 2020/02/23 06:00 [pubmed]
PHST- 2020/02/23 06:01 [medline]
PHST- 2020/02/01 00:00 [pmc-release]
AID - tard-48-1-68 [pii]
AID - 10.5152/TJAR.2019.90522 [doi]
PST - ppublish
SO  - Turk J Anaesthesiol Reanim. 2020 Feb;48(1):68-70. doi: 10.5152/TJAR.2019.90522. 
      Epub 2019 Nov 11.