PMID- 34261427 OWN - NLM STAT- MEDLINE DCOM- 20220404 LR - 20221207 IS - 1743-1328 (Electronic) IS - 0161-6412 (Linking) VI - 44 IP - 1 DP - 2022 Jan TI - Incidence and prevalence of neuromyelitis optica spectrum disorders in Slovakia. PG - 38-46 LID - 10.1080/01616412.2021.1952741 [doi] AB - OBJECTIVE: : Neuromyelitis optica spectrum disorders (NMOSDs) are a group of rare, inflammatory, demyelinating diseases that affect the central nervous system. Neither the incidence nor the prevalence of NMOSD has been determined in Slovakia thus far. The aim of this study was to determine both the incidence and the prevalence of NMOSD in Slovakia using the 2015 International Panel of NMOSD diagnosis (IPND) criteria. METHODS: : We performed a population-based study in Slovakia to estimate both the incidence and the prevalence of NMOSD during the period from 1 January 2006 through 31 December 2019. NMOSD cases were reported from multiple sources and the diagnosis was subsequently verified using the IPND criteria by a joint commitee of three neurologists. The prevalence is reported as number of cases per 100,000 inhabitans and the incidence as number of new cases per 1,000,000 person-years. Age-adjusted rates to the WHO standard population 2005-2025 were also calculated. RESULTS: : We identified 63 NMOSD cases. The crude point-prevalence rate was 1.37 (95% CI 1.03-1.71) per 100,000 inhabitants. The crude indidence rate was 0.88 (95% CI 0.65-1.12) per 1,000,000 person-years. The age-adjusted point-prevalence rate was 1.42 (95% CI 1.07-1.84) per 100,000 persons and the age-adjusted incidence rate was 0.96 (95% CI 0.72-1.25) per 1,000,000 person-years. CONCLUSION: : The NMOSD epidemiological situation in Slovakia is comparable to those reported from other Caucasian populations. FAU - Szilasiova, Jarmila AU - Szilasiova J AD - Department of Neurology, Pavol Jozef Safarik University, Kosice, Slovak Republic. FAU - Gazda, Jakub AU - Gazda J AD - II Department of Internal Medicine, Pavol Jozef Safarik University, Kosice, Slovak Republic. FAU - Cimprichova, Andrea AU - Cimprichova A AD - Department of Neurology, Faculty Hospital, Trencin, Slovak Republic. FAU - Cvengrosova, Anna AU - Cvengrosova A AD - Department of Neurology, J. A. Reiman Faculty Hospital, Presov, Slovak Republic. FAU - Donath, Vladimir AU - Donath V AD - Department of Neurology, F. D. Roosevelt Faculty Hospital, Banska Bystrica, Slovak Republic. FAU - Fedicova, Miriam AU - Fedicova M AUID- ORCID: 0000-0002-3118-6501 AD - Department of Neurology, L. Pasteur University Hospital, Kosice, Slovak Republic. FAU - Gurcik, Ladislav AU - Gurcik L AD - Department of Neurology, AGEL Hospital, Levoca, Slovak Republic. FAU - Hancinova, Viera AU - Hancinova V AD - Department of Neurology, University Hospital, Bratislava Ruzinov, Slovak Republic. FAU - Jurcaga, Frantisek AU - Jurcaga F AD - Department of Neurology, St. Michal University Hospital, Bratislava, Slovak Republic. FAU - Kahancova, Edita AU - Kahancova E AD - Department of Neurology, L. Pasteur University Hospital, Kosice, Slovak Republic. FAU - Kantorova, Ema AU - Kantorova E AD - Department of Neurology, University Hospital, Martin, Slovak Republic. FAU - Karlik, Martin AU - Karlik M AD - Department of Neurology, L. Derer University Hospital Bratislava, Slovak Republic. FAU - Klimova, Eleonora AU - Klimova E AD - Department of Neurology, J. A. Reiman Faculty Hospital, Presov, Slovak Republic. FAU - Kovacova, Slavomira AU - Kovacova S AD - Department of Neurology, Faculty Hospital, Nitra, Slovak Republic. FAU - Krastev, Georgi AU - Krastev G AD - Department of Neurology, Faculty Hospital, Trnava, Slovak Republic. FAU - Megova, Andrea AU - Megova A AD - Department of Neurology, University Hospital, Bratislava, Slovak Republic. FAU - Michalik, Jozef AU - Michalik J AD - Department of Neurology, University Hospital, Martin, Slovak Republic. FAU - Mikula, Pavol AU - Mikula P AD - Department of Social and Behavioral Medicine, Pavol Jozef Safarik University, Kosice, Slovak Republic. FAU - Snopekova, Lubica AU - Snopekova L AD - Department of Neurology, Hospital Poprad, Poprad, Slovak Republic. FAU - Stevkova, Zuzana AU - Stevkova Z AD - Department of Neurology, Faculty Hospital, Trnava, Slovak Republic. LA - eng PT - Journal Article DEP - 20210714 PL - England TA - Neurol Res JT - Neurological research JID - 7905298 RN - 0 (Aquaporin 4) RN - 0 (Autoantibodies) SB - IM MH - Aquaporin 4 MH - Autoantibodies MH - Humans MH - Incidence MH - *Neuromyelitis Optica/diagnosis/epidemiology MH - Prevalence MH - Slovakia/epidemiology MH - White People OTO - NOTNLM OT - AQP4 OT - Neuromyelitis optica spectrum disorders OT - Slovakia population-based study OT - incidence OT - prevalence EDAT- 2021/07/16 06:00 MHDA- 2022/04/05 06:00 CRDT- 2021/07/15 05:28 PHST- 2021/07/16 06:00 [pubmed] PHST- 2022/04/05 06:00 [medline] PHST- 2021/07/15 05:28 [entrez] AID - 10.1080/01616412.2021.1952741 [doi] PST - ppublish SO - Neurol Res. 2022 Jan;44(1):38-46. doi: 10.1080/01616412.2021.1952741. Epub 2021 Jul 14.