PMID- 34262809 OWN - NLM STAT- PubMed-not-MEDLINE LR - 20231107 IS - 2168-8184 (Print) IS - 2168-8184 (Electronic) IS - 2168-8184 (Linking) VI - 13 IP - 6 DP - 2021 Jun TI - Kawasaki Disease Shock Syndrome: A Nine-Year-Old Girl With Atypical Presentation of Kawasaki Disease in Emergency Department. PG - e15471 LID - 10.7759/cureus.15471 [doi] LID - e15471 AB - Kawasaki disease (KD) is an acute rheumatological illness usually affecting children between six months and five years of age. It is a vasculitis syndrome of medium-sized vessels that has typical clinical characteristics such as fever, rash, cervical lymphadenopathy, conjunctivitis, and mucosal changes. However, sometimes, it may present with the features of shock when it is known as Kawasaki disease shock syndrome (KDSS). The actual etiology of this disease is still unknown. The primary treatment of this disease is aspirin and intravenous immunoglobulin (IVIG). The most common and serious complication of KD is cardiac complications which can be avoided by IVIG if given on time. KDSS is the other rare but serious early complication that can be presented to the ED as an initial presenting feature. Early diagnosis of KDSS in the ED and its treatment is very important to prevent early and late complications, including cardiac complications of this disease. Although the usual age group for this disease is under five years, here we have presented a rare case of KDSS in a nine-year-old female child. CI - Copyright (c) 2021, Shah et al. FAU - Shah, Sunil AU - Shah S AD - Medicine, California Institute of Behavioral Neurosciences & Psychology, Fairfield, USA. AD - Medicine, Ministry of Health, Male, MDV. FAU - Karki, Divya AU - Karki D AD - Pediatrics, Ministry of Health, Male, MDV. FAU - Gami, Sumit AU - Gami S AD - Medicine, Universal College of Medical Sciences, Bhairahawa, NPL. AD - Internal Medicine, Nidan Hospital, Lalitpur, NPL. FAU - Panth, Himal AU - Panth H AD - Medicine, Universal College of Medical Sciences, Bhairahawa, NPL. FAU - Neupane, Nischal AU - Neupane N AD - Pediatrics, Ministry of Health, Male, MDV. LA - eng PT - Case Reports DEP - 20210605 PL - United States TA - Cureus JT - Cureus JID - 101596737 PMC - PMC8260190 OTO - NOTNLM OT - kawasaki disease OT - kawasaki disease shock syndrome OT - shock OT - systemic inflammation OT - vasculitis COIS- The authors have declared that no competing interests exist. EDAT- 2021/07/16 06:00 MHDA- 2021/07/16 06:01 PMCR- 2021/06/05 CRDT- 2021/07/15 06:22 PHST- 2021/06/05 00:00 [accepted] PHST- 2021/07/15 06:22 [entrez] PHST- 2021/07/16 06:00 [pubmed] PHST- 2021/07/16 06:01 [medline] PHST- 2021/06/05 00:00 [pmc-release] AID - 10.7759/cureus.15471 [doi] PST - epublish SO - Cureus. 2021 Jun 5;13(6):e15471. doi: 10.7759/cureus.15471. eCollection 2021 Jun.