PMID- 38343272 OWN - NLM STAT- Publisher LR - 20240212 IS - 1439-7609 (Electronic) IS - 1439-7595 (Linking) DP - 2024 Feb 7 TI - Nationwide epidemiological survey of polyarteritis nodosa in Japan in 2020. LID - roae010 [pii] LID - 10.1093/mr/roae010 [doi] AB - Polyarteritis nodosa (PAN) is a systemic necrotizing vasculitis that predominantly affects medium-sized arteries. With advances in our understanding of the pathogenesis and classification of vasculitis, PAN and microscopic polyangiitis (MPA), a disease of anti-neutrophil cytoplasmic antibody-associated vasculitis (AAV), were separated from the group of diseases previously diagnosed as periarteritis nodosa (PN) at the Chapel Hill Consensus Conference (CHCC) in 1994 (1). CI - (c) Japan College of Rheumatology 2024. Published by Oxford University Press. All rights reserved. For permissions, please e-mail: journals.permissions@oup.com. FAU - Kawazoe, Mai AU - Kawazoe M AUID- ORCID: 0000-0002-9822-8067 AD - Division of Rheumatology, Department of Internal Medicine, School of Medicine, Faculty of Medicine, Toho University, Tokyo, Japan. FAU - Nanki, Toshihiro AU - Nanki T AUID- ORCID: 0000-0002-3482-074X AD - Division of Rheumatology, Department of Internal Medicine, School of Medicine, Faculty of Medicine, Toho University, Tokyo, Japan. FAU - Saeki, Keigo AU - Saeki K AD - Department of Epidemiology, Nara University School of Medicine, Nara, Japan. FAU - Ishikawa, Hideki AU - Ishikawa H AD - Department of Molecular-Targeting Prevention, Graduate School of Medical Science, Kyoto Prefectural University of Medicine, Kyoto, Japan. FAU - Nakamura, Yoshikazu AU - Nakamura Y AD - Department of Public Health, Jichi Medical University, Tochigi, Japan. FAU - Kawashima, Soko AU - Kawashima S AD - Department of Nephrology and Rheumatology, Kyorin University School of Medicine, Tokyo, Japan. FAU - Ito, Shuichi AU - Ito S AUID- ORCID: 0000-0002-5242-8987 AD - Department of Pediatrics, Graduate School of Medicine, Yokohama City University, Yokohama, Japan. FAU - Kodera, Masanari AU - Kodera M AD - Department of Dermatology, Japan Community Health Care Organization Chukyo Hospital, Aichi, Japan. FAU - Konda, Naoko AU - Konda N AD - Division of Rheumatology, Department of Internal Medicine, Tokyo Women's Medical University School of Medicine, Tokyo, Japan. FAU - Kaname, Shinya AU - Kaname S AD - Department of Nephrology and Rheumatology, Kyorin University School of Medicine, Tokyo, Japan. FAU - Harigai, Masayoshi AU - Harigai M AUID- ORCID: 0000-0002-6418-2603 AD - Division of Rheumatology, Department of Internal Medicine, Tokyo Women's Medical University School of Medicine, Tokyo, Japan. LA - eng PT - Journal Article DEP - 20240207 PL - England TA - Mod Rheumatol JT - Modern rheumatology JID - 100959226 SB - IM OTO - NOTNLM OT - Japan OT - epidemiology OT - polyarteritis nodosa OT - prevalence OT - systemic vasculitis EDAT- 2024/02/12 15:42 MHDA- 2024/02/12 15:42 CRDT- 2024/02/12 02:43 PHST- 2023/10/13 00:00 [received] PHST- 2023/12/11 00:00 [revised] PHST- 2024/02/05 00:00 [accepted] PHST- 2024/02/12 15:42 [medline] PHST- 2024/02/12 15:42 [pubmed] PHST- 2024/02/12 02:43 [entrez] AID - 7606450 [pii] AID - 10.1093/mr/roae010 [doi] PST - aheadofprint SO - Mod Rheumatol. 2024 Feb 7:roae010. doi: 10.1093/mr/roae010.