PMID- 6576612 OWN - NLM STAT- MEDLINE DCOM- 19830920 LR - 20190821 IS - 0001-656X (Print) IS - 0001-656X (Linking) VI - 72 IP - 3 DP - 1983 May TI - Hereditary motor and sensory neuropathies in Swedish children. I. Prevalence and distribution by disability groups. PG - 379-83 AB - The prevalence of hereditary motor and sensory neuropathies (HMSN) and their distribution according to the severity of the disability were studied in a population-based series of Swedish children 2-15 years old. The prevalence per 100 000 of total peroneal muscle atrophies was 21.6 and of all clinical HMSN 19.0 Among HMSN, de- and remyelinating types (HMSN I) constituted 8 per 100000 and neuronal-axonal types (HMSN II) 11. Eighteen of the 21 HMSN I cases and 26 of the 29 HMSN II were considered to represent an autosomal dominant mode of inheritance. Ten per cent of all children were severely, 70% moderately and 20% mildly disabled. All the severely affected children belonged to the HMSN I group and 9 of the 10 mildly affected to HMSN II. FAU - Hagberg, B AU - Hagberg B FAU - Westerberg, B AU - Westerberg B LA - eng PT - Journal Article PT - Research Support, Non-U.S. Gov't PL - Sweden TA - Acta Paediatr Scand JT - Acta paediatrica Scandinavica JID - 0000211 SB - IM MH - Adolescent MH - Child MH - Child, Preschool MH - Female MH - Hereditary Sensory and Autonomic Neuropathies/*epidemiology/genetics MH - Humans MH - Male MH - Muscular Atrophy/epidemiology MH - Neuromuscular Diseases/*epidemiology/genetics MH - Sweden EDAT- 1983/05/01 00:00 MHDA- 1983/05/01 00:01 CRDT- 1983/05/01 00:00 PHST- 1983/05/01 00:00 [pubmed] PHST- 1983/05/01 00:01 [medline] PHST- 1983/05/01 00:00 [entrez] AID - 10.1111/j.1651-2227.1983.tb09732.x [doi] PST - ppublish SO - Acta Paediatr Scand. 1983 May;72(3):379-83. doi: 10.1111/j.1651-2227.1983.tb09732.x.