PMID- 9080158
OWN - NLM
STAT- MEDLINE
DCOM- 19970612
LR  - 20190512
IS  - 1010-7940 (Print)
IS  - 1010-7940 (Linking)
VI  - 11
IP  - 2
DP  - 1997 Feb
TI  - Congenital aortopulumonary window: diagnosis, surgical technique and long-term 
      results.
PG  - 293-7
AB  - OBJECTIVE: Congenital aortopulmonary window is rare, often associated with other 
      cardiac anomalies. Surgical repair as the only treatment should be performed 
      before pulmonary vascular changes have developed. This study presents the 
      long-term outcome after surgical correction for this condition. MATERIALS AND 
      METHODS: Between 1971 and 1993, 13 patients with congenital aortopulmonary window 
      were found. 10 had type I, 2 type II and 1 had type III. Concomitant cardiac 
      anomalies were present in 10/13. Eleven patients were operated on at a mean age 
      of 31.2 +/- 48.3 months (range 6 days-10 years). Thoracotomy was used in 3 and 
      sternotomy in 9 patients. In 4/11, the aorto-pulmonary window was simply ligated, 
      4 had a transpulmonary approach and 1 combined with a transaortic approach. The 
      aortopulmonary window was closed directly in 2 and with a Dacron patch in 1. 
      Cardiopulmonary bypass was used in 6 patients. Associated anomalies in 10/11 
      patients. RESULTS: There was one operative death (9%): a six-day old boy with 
      interrupted aortic arch died 6 h postoperatively due to low-cardiac output. The 
      mean follow-up period is 8.1 +/- 7.3 years (range 2-24 years). Clinical 
      examination, transaortic echocardiography and/or cardiac catheterization were 
      obtained in the follow-up. There was no late death. All are in New York Heart 
      Association (NYHA) class I. One had to be reoperated on for a recurrent shunt 29 
      months after ligation and one had angioplasty after 23 months for residual 
      stenosis of the reimplanted right pulmonary artery. The actuarial survival rate 
      is 90% after 1, 5 and 10 years. CONCLUSIONS: The surgical treatment of 
      aortopulmonary window has a low risk, even if associated with major cardiac 
      anomalies. Prompt operative treatment achieves excellent long-term results.
FAU - Tkebuchava, T
AU  - Tkebuchava T
AD  - Clinic for Cardiovascular Surgery, University Hospital, Zurich, Switzerland.
FAU - von Segesser, L K
AU  - von Segesser LK
FAU - Vogt, P R
AU  - Vogt PR
FAU - Bauersfeld, U
AU  - Bauersfeld U
FAU - Jenni, R
AU  - Jenni R
FAU - Kunzli, A
AU  - Kunzli A
FAU - Lachat, M
AU  - Lachat M
FAU - Turina, M
AU  - Turina M
LA  - eng
PT  - Journal Article
PL  - Germany
TA  - Eur J Cardiothorac Surg
JT  - European journal of cardio-thoracic surgery : official journal of the European 
      Association for Cardio-thoracic Surgery
JID - 8804069
SB  - IM
MH  - Actuarial Analysis
MH  - Aortopulmonary Septal Defect/classification/mortality/*surgery
MH  - Child
MH  - Child, Preschool
MH  - Exercise Test
MH  - Female
MH  - Follow-Up Studies
MH  - Heart Defects, Congenital/classification/mortality/surgery
MH  - Hemodynamics/physiology
MH  - Humans
MH  - Infant
MH  - Infant, Newborn
MH  - Male
MH  - Postoperative Complications/classification/mortality/surgery
MH  - Reoperation
MH  - Survival Rate
EDAT- 1997/02/01 00:00
MHDA- 1997/02/01 00:01
CRDT- 1997/02/01 00:00
PHST- 1997/02/01 00:00 [pubmed]
PHST- 1997/02/01 00:01 [medline]
PHST- 1997/02/01 00:00 [entrez]
AID - S1010794096010482 [pii]
AID - 10.1016/s1010-7940(96)01048-2 [doi]
PST - ppublish
SO  - Eur J Cardiothorac Surg. 1997 Feb;11(2):293-7. doi: 
      10.1016/s1010-7940(96)01048-2.