PMID- 19129235 OWN - NLM STAT- MEDLINE DCOM- 20090417 LR - 20211203 IS - 1362-4962 (Electronic) IS - 0305-1048 (Print) IS - 0305-1048 (Linking) VI - 37 IP - 6 DP - 2009 Apr TI - A role for monoubiquitinated FANCD2 at telomeres in ALT cells. PG - 1740-54 LID - 10.1093/nar/gkn995 [doi] AB - Both Fanconi anemia (FA) and telomere dysfunction are associated with chromosome instability and an increased risk of cancer. Because of these similarities, we have investigated whether there is a relationship between the FA protein, FANCD2 and telomeres. We find that FANCD2 nuclear foci colocalize with telomeres and PML bodies in immortalized telomerase-negative cells. These cells maintain telomeres by alternative lengthening of telomeres (ALT). In contrast, FANCD2 does not colocalize with telomeres or PML bodies in cells which express telomerase. Using a siRNA approach we find that FANCA and FANCL, which are components of the FA nuclear core complex, regulate FANCD2 monoubiquitination and the telomeric localization of FANCD2 in ALT cells. Transient depletion of FANCD2, or FANCA, results in a dramatic loss of detectable telomeres in ALT cells but not in telomerase-expressing cells. Furthermore, telomere loss following depletion of these proteins in ALT cells is associated with decreased homologous recombination between telomeres (T-SCE). Thus, the FA pathway has a novel function in ALT telomere maintenance related to DNA repair. ALT telomere maintenance is therefore one mechanism by which monoubiquitinated FANCD2 may promote genetic stability. FAU - Fan, Qiang AU - Fan Q AD - Division of Experimental Hematology and Cancer Biology, Cincinnati Children's Research Foundation, Department of Pediatrics, University of Cincinnati College of Medicine, Cincinnati, OH 45229, USA. FAU - Zhang, Fan AU - Zhang F FAU - Barrett, Briana AU - Barrett B FAU - Ren, Keqin AU - Ren K FAU - Andreassen, Paul R AU - Andreassen PR LA - eng GR - R01 HL085587/HL/NHLBI NIH HHS/United States PT - Journal Article PT - Research Support, N.I.H., Extramural PT - Research Support, Non-U.S. Gov't DEP - 20090107 PL - England TA - Nucleic Acids Res JT - Nucleic acids research JID - 0411011 RN - 0 (Cell Cycle Proteins) RN - 0 (Fanconi Anemia Complementation Group A Protein) RN - 0 (Fanconi Anemia Complementation Group D2 Protein) RN - 0 (Telomeric Repeat Binding Protein 1) RN - EC 2.3.2.27 (Fanconi Anemia Complementation Group L Protein) RN - EC 2.7.11.1 (ATR protein, human) RN - EC 2.7.11.1 (Ataxia Telangiectasia Mutated Proteins) RN - EC 2.7.11.1 (Protein Serine-Threonine Kinases) SB - IM MH - Ataxia Telangiectasia Mutated Proteins MH - Cell Cycle Proteins/physiology MH - Cell Line MH - Cell Line, Transformed MH - Fanconi Anemia Complementation Group A Protein/antagonists & inhibitors/physiology MH - Fanconi Anemia Complementation Group D2 Protein/analysis/antagonists & inhibitors/*metabolism MH - Fanconi Anemia Complementation Group L Protein/physiology MH - HeLa Cells MH - Humans MH - Protein Serine-Threonine Kinases/physiology MH - Sister Chromatid Exchange MH - Telomere/chemistry/*metabolism MH - Telomeric Repeat Binding Protein 1/analysis MH - *Ubiquitination PMC - PMC2665210 EDAT- 2009/01/09 09:00 MHDA- 2009/04/18 09:00 PMCR- 2009/01/07 CRDT- 2009/01/09 09:00 PHST- 2009/01/09 09:00 [entrez] PHST- 2009/01/09 09:00 [pubmed] PHST- 2009/04/18 09:00 [medline] PHST- 2009/01/07 00:00 [pmc-release] AID - gkn995 [pii] AID - 10.1093/nar/gkn995 [doi] PST - ppublish SO - Nucleic Acids Res. 2009 Apr;37(6):1740-54. doi: 10.1093/nar/gkn995. Epub 2009 Jan 7.